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anti-Acyl-CoA Dehydrogenase, Very Long Chain (ACADVL) Antibodies

The protein encoded by ACADVL is targeted to the inner mitochondrial membrane where it catalyzes the first step of the mitochondrial fatty acid beta-oxidation pathway. Additionally we are shipping ACADVL Proteins (13) and many more products for this protein.

list all antibodies Gene Name GeneID UniProt
ACADVL 37 P49748
ACADVL 25363 P45953
ACADVL 11370 P50544
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Top anti-ACADVL Antibodies at antibodies-online.com

Showing 10 out of 71 products:

Catalog No. Reactivity Host Conjugate Application Images Quantity Supplier Delivery Price Details
Cow Rabbit Un-conjugated WB WB Suggested Anti-ACADVL Antibody Titration: 0.2-1 ug/mlPositive Control: HepG2 cell lysate 100 μL Log in to see 2 to 3 Days
$289.00
Details
Human Goat Un-conjugated EIA, WB AP23726PU-N VLCAD antibody staining of Human Heart lysate at 2 µg/ml (35µg protein in RIPA buffer). Primary incubation was 1 hour. Detected by chemiluminescence. 0.1 mg Log in to see 6 to 8 Days
$379.50
Details
Human Mouse Un-conjugated WB ACADVL monoclonal antibody (M01), clone 5D3 Western Blot analysis of ACADVL expression in Hela NE on formalin-fixed paraffin-embedded human heart (antibody concentration 3 µg/mL). 0.1 mg Log in to see 8 to 11 Days
$450.00
Details
Human Rabbit Un-conjugated WB WB Suggested Anti-ACADVL Antibody Titration: 0.2-1 ug/mlELISA Titer: 1:1562500Positive Control: ACHN cell lysate WB Suggested Anti-ACADVL  Antibody Titration: 0.2-1 µg/mL ELISA Titer: 1:1562500  Positive Control: ACHN cell lysate  ACADVL is supported by BioGPS gene expression data to be expressed in ACHN 100 μL Log in to see 2 to 3 Days
$289.00
Details
Human Rabbit Un-conjugated WB 100 μg Log in to see 2 to 3 Days
$283.50
Details
Human Mouse Un-conjugated IHC (p), ELISA, WB Immunoperoxidase of monoclonal antibody to ACADVL on formalin-fixed paraffin-embedded human heart. [antibody concentration 3 ug/ml] ACADVL monoclonal antibody (M01), clone 5D3 Western Blot analysis of ACADVL expression in Hela S3 NE . 100 μg Log in to see 9 Days
$430.00
Details
Human Goat Un-conjugated ELISA, WB 0.1 mg Log in to see 2 to 3 Days
$433.13
Details
Human Goat Un-conjugated ELISA, WB ABIN1589990 (1 µg/mL) staining of Human Heart lysate (35 µg protein in RIPA buffer). Primary incubation was 1 hour. Detected by chemiluminescence. 100 μg Log in to see 4 to 5 Days
$318.20
Details
Human Rabbit Un-conjugated WB 50 μg Log in to see 8 to 10 Days
$551.83
Details
Human Rabbit Un-conjugated ELISA, WB 50 μg Log in to see 2 to 3 Days
$433.13
Details

ACADVL Antibodies by Reactivity, Application, Clonality and Conjugate

Attributes Applications Host Clonality Conjugate
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Top referenced anti-ACADVL Antibodies

  1. Human Monoclonal ACADVL Primary Antibody for WB - ABIN396579 : Pan, Chen, Pan, Wang, Han, Zheng, Wang, Li, Qu, Shao: Differential gene expression identified in Uigur women cervical squamous cell carcinoma by suppression subtractive hybridization. in Neoplasma 2010 (PubMed)
    Show all 5 references for ABIN396579

  2. Cow (Bovine) Polyclonal ACADVL Primary Antibody for WB - ABIN2785735 : Soon, Libe, Benn, Gill, Shaw, Sywak, Groussin, Bertagna, Gicquel, Bertherat, McDonald, Sidhu, Robinson: Loss of heterozygosity of 17p13, with possible involvement of ACADVL and ALOX15B, in the pathogenesis of adrenocortical tumors. in Annals of surgery 2007 (PubMed)
    Show all 2 references for ABIN2785735

  3. Human Monoclonal ACADVL Primary Antibody for IHC (p), ELISA - ABIN559746 : De Pauw, Demine, Tejerina, Dieu, Delaive, Kel, Renard, Raes, Arnould: Mild mitochondrial uncoupling does not affect mitochondrial biogenesis but downregulates pyruvate carboxylase in adipocytes: role for triglyceride content reduction. in American journal of physiology. Endocrinology and metabolism 2012 (PubMed)
    Show all 2 references for ABIN559746

  4. Human Polyclonal ACADVL Primary Antibody for EIA, WB - ABIN615945 : Gobin-Limballe, Djouadi, Aubey, Olpin, Andresen, Yamaguchi, Mandel, Fukao, Ruiter, Wanders, McAndrew, Kim, Bastin: Genetic basis for correction of very-long-chain acyl-coenzyme A dehydrogenase deficiency by bezafibrate in patient fibroblasts: toward a genotype-based therapy. in American journal of human genetics 2007 (PubMed)

More Antibodies against ACADVL Interaction Partners

Human Acyl-CoA Dehydrogenase, Very Long Chain (ACADVL) interaction partners

  1. 11 mutations in ACADVL gene in 7 patients, 7 reported (p.S22X, p.W427X, p.A213T, p.G222R, p.R450H, c.296-297delCA, c.1605+1G>T), 4 novel (p.S72F, p.Q100X, p.M437T, p.D466Y). p.R450H and p.D466Y (14.28%, 2/14 alleles) mutations identified in 2 alleles.

  2. Case Report: missense mutation within the ACADVL gene responsible for very-long-chain acyl-CoA dehydrogenase deficiency and sudden infant death.

  3. These results emphasize the importance of functional investigation of abnormal NBS (show NBN Antibodies) or clinical testing suggestive but not diagnostic of very-long-chain acyl-CoA dehydrogenase .

  4. These findings support the importance of considering that mutations may be present in the ACADVL gene when a significant partial deficiency is found in CPTII (show CPT2 Antibodies) activity, but no mutations in the CPT2 (show CPT2 Antibodies) gene can be identified.

  5. Identification of 2 VLCAD mutations leads to precautions in the management of the children with VLCAD deficiency.

  6. The expressions of LCHAD (show HADHA Antibodies) gene and protein are remarkably reduced in early onset severe preeclampsia and HELLP syndrome.

  7. Analyzed potential rhabdomyolysis-susceptibility genes (RYR 1 (show RYR1 Antibodies), CPT II (show CPT2 Antibodies), VLCAD and CYP (show PPIG Antibodies) 2D6) from autopsy samples of methamphetamine abusers; no obvious relationship between the genetic mutations observed in this study and rhabdomyolysis was seen.

  8. Down regulation of ACADVL is associated with cervical squamous cell carcinoma.

  9. Missense mutations in Very-Long-Chain Acyl-CoA Dehydrogenase is associated with inborn errors of lipid metabolism.

  10. This study confirms that VLCAD deficiency, although being less frequent than CPT II (show CPT2 Antibodies) deficiency, should be systematically considered in the differential diagnosis of exercise-induced rhabdomyolysis.

Cow (Bovine) Acyl-CoA Dehydrogenase, Very Long Chain (ACADVL) interaction partners

  1. Bovine ACADVL gene had a significant effect on chest width (P<0.05), chest depth (P<0.05), and hip width (P<0.05) in the Qinchuan breed.

Mouse (Murine) Acyl-CoA Dehydrogenase, Very Long Chain (ACADVL) interaction partners

  1. observed strong upregulation of peroxisomal beta-oxidation in VLCAD(-/-) mice

  2. SIRT3 (show SIRT3 Antibodies) and SIRT5 (show SIRT5 Antibodies) regulate the enzyme activity and cardiolipin binding of very long-chain acyl-CoA dehydrogenase

  3. Studies conducted with permeabilized mitochondria and different chain length acyl-CoA (show GNPAT Antibodies) derivatives suggest that VLCAD is also a source of reactive oxygen species production in mitochondria of high fat diet animals.

  4. We demonstrate here that both dietary interventions with respect to the fat content of the diet reverse endogenous compensatory mechanisms in muscle that have evolved in VLCAD(-/-) mice resulting in pronounced energy deficiency

  5. VLCAD(-/-) mice develop tissue-specific strategies to compensate deficiency of VLCAD either by induction of other mitochondrial acyl-CoA (show GNPAT Antibodies) dehydrogenases or by enhancement of glucose oxidation.

  6. Report a longer QTc interval and lipid alterations in VLCAD null mice.

  7. Four VLCAD-/- deficient mice died unexpectedly on the treadmill during the early stages of training. The VLCAD-/- deficient mice that survived adapted to the aerobic interval training similarly to the non-deficient mice.

  8. Medium-chain triglycerides impair lipid metabolism and induce hepatic steatosis in very long-chain acyl-CoA dehydrogenase (VLCAD)-deficient mice

  9. Data show that in VLCAD knockout mice fed a long-chain triglyceride diet, fasting results in accumulation of liver lipids, hepatopathy and upregulation of peroxisomal and microsomal oxidation pathways as well as antioxidant enzyme activities and TBARS.

  10. medium-chain triglyceride application prevents acylcarnitine accumulation in skeletal muscle from very-long-chain acyl-CoA-dehydrogenase-deficient mice

ACADVL Antigen Profile

Protein Summary

The protein encoded by this gene is targeted to the inner mitochondrial membrane where it catalyzes the first step of the mitochondrial fatty acid beta-oxidation pathway. This acyl-Coenzyme A dehydrogenase is specific to long-chain and very-long-chain fatty acids. A deficiency in this gene product reduces myocardial fatty acid beta-oxidation and is associated with cardiomyopathy. Alternative splicing results in multiple transcript variants encoding different isoforms.

Gene names and symbols associated with ACADVL

  • acyl-CoA dehydrogenase, very long chain (ACADVL) antibody
  • acyl-CoA dehydrogenase, very long chain (Acadvl) antibody
  • acyl-Coenzyme A dehydrogenase, very long chain (acadvl) antibody
  • acyl-Coenzyme A dehydrogenase, very long chain (Acadvl) antibody
  • ACAD6 antibody
  • fb52d04 antibody
  • LCACD antibody
  • vlcad antibody
  • wu:fb52d04 antibody
  • wu:fc75e01 antibody
  • zgc:64067 antibody

Protein level used designations for ACADVL

acyl-Coenzyme A dehydrogenase, very long chain , very long-chain specific acyl-CoA dehydrogenase, mitochondrial , VLCAD , acyl-coenzyme A dehydrogenase, very long chain , VLCAD very-long-chain acyl-CoA dehydrogenase , Very long chain Acyl-Coa dehydrogenase , vlcad , MVLCAD

GENE ID SPECIES
100061583 Equus caballus
37 Homo sapiens
489463 Canis lupus familiaris
282130 Bos taurus
25363 Rattus norvegicus
573723 Danio rerio
11370 Mus musculus
Selected quality suppliers for anti-ACADVL (ACADVL) Antibodies
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