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Acyl-CoA Dehydrogenase, Very Long Chain (ACADVL) ELISA Kits

The protein encoded by ACADVL is targeted to the inner mitochondrial membrane where it catalyzes the first step of the mitochondrial fatty acid beta-oxidation pathway. Additionally we are shipping ACADVL Antibodies (71) and ACADVL Proteins (13) and many more products for this protein.

list all ELISA KIts Gene Name GeneID UniProt
Anti-Human ACADVL ACADVL 37 P49748
Anti-Rat ACADVL ACADVL 25363 P45953
Anti-Mouse ACADVL ACADVL 11370 P50544
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More ELISA Kits for ACADVL Interaction Partners

Human Acyl-CoA Dehydrogenase, Very Long Chain (ACADVL) interaction partners

  1. 11 mutations in ACADVL gene in 7 patients, 7 reported (p.S22X, p.W427X, p.A213T, p.G222R, p.R450H, c.296-297delCA, c.1605+1G>T), 4 novel (p.S72F, p.Q100X, p.M437T, p.D466Y). p.R450H and p.D466Y (14.28%, 2/14 alleles) mutations identified in 2 alleles.

  2. Case Report: missense mutation within the ACADVL gene responsible for very-long-chain acyl-CoA dehydrogenase deficiency and sudden infant death.

  3. These results emphasize the importance of functional investigation of abnormal NBS (show NBN ELISA Kits) or clinical testing suggestive but not diagnostic of very-long-chain acyl-CoA dehydrogenase .

  4. These findings support the importance of considering that mutations may be present in the ACADVL gene when a significant partial deficiency is found in CPTII (show CPT2 ELISA Kits) activity, but no mutations in the CPT2 (show CPT2 ELISA Kits) gene can be identified.

  5. Identification of 2 VLCAD mutations leads to precautions in the management of the children with VLCAD deficiency.

  6. The expressions of LCHAD (show HADHA ELISA Kits) gene and protein are remarkably reduced in early onset severe preeclampsia and HELLP syndrome.

  7. Analyzed potential rhabdomyolysis-susceptibility genes (RYR 1 (show RYR1 ELISA Kits), CPT II (show CPT2 ELISA Kits), VLCAD and CYP (show PPIG ELISA Kits) 2D6) from autopsy samples of methamphetamine abusers; no obvious relationship between the genetic mutations observed in this study and rhabdomyolysis was seen.

  8. Down regulation of ACADVL is associated with cervical squamous cell carcinoma.

  9. Missense mutations in Very-Long-Chain Acyl-CoA Dehydrogenase is associated with inborn errors of lipid metabolism.

  10. This study confirms that VLCAD deficiency, although being less frequent than CPT II (show CPT2 ELISA Kits) deficiency, should be systematically considered in the differential diagnosis of exercise-induced rhabdomyolysis.

Cow (Bovine) Acyl-CoA Dehydrogenase, Very Long Chain (ACADVL) interaction partners

  1. Bovine ACADVL gene had a significant effect on chest width (P<0.05), chest depth (P<0.05), and hip width (P<0.05) in the Qinchuan breed.

Mouse (Murine) Acyl-CoA Dehydrogenase, Very Long Chain (ACADVL) interaction partners

  1. observed strong upregulation of peroxisomal beta-oxidation in VLCAD(-/-) mice

  2. SIRT3 (show SIRT3 ELISA Kits) and SIRT5 (show SIRT5 ELISA Kits) regulate the enzyme activity and cardiolipin binding of very long-chain acyl-CoA dehydrogenase

  3. Studies conducted with permeabilized mitochondria and different chain length acyl-CoA (show GNPAT ELISA Kits) derivatives suggest that VLCAD is also a source of reactive oxygen species production in mitochondria of high fat diet animals.

  4. We demonstrate here that both dietary interventions with respect to the fat content of the diet reverse endogenous compensatory mechanisms in muscle that have evolved in VLCAD(-/-) mice resulting in pronounced energy deficiency

  5. VLCAD(-/-) mice develop tissue-specific strategies to compensate deficiency of VLCAD either by induction of other mitochondrial acyl-CoA (show GNPAT ELISA Kits) dehydrogenases or by enhancement of glucose oxidation.

  6. Report a longer QTc interval and lipid alterations in VLCAD null mice.

  7. Four VLCAD-/- deficient mice died unexpectedly on the treadmill during the early stages of training. The VLCAD-/- deficient mice that survived adapted to the aerobic interval training similarly to the non-deficient mice.

  8. Medium-chain triglycerides impair lipid metabolism and induce hepatic steatosis in very long-chain acyl-CoA dehydrogenase (VLCAD)-deficient mice

  9. Data show that in VLCAD knockout mice fed a long-chain triglyceride diet, fasting results in accumulation of liver lipids, hepatopathy and upregulation of peroxisomal and microsomal oxidation pathways as well as antioxidant enzyme activities and TBARS.

  10. medium-chain triglyceride application prevents acylcarnitine accumulation in skeletal muscle from very-long-chain acyl-CoA-dehydrogenase-deficient mice

ACADVL Antigen Profile

Antigen Summary

The protein encoded by this gene is targeted to the inner mitochondrial membrane where it catalyzes the first step of the mitochondrial fatty acid beta-oxidation pathway. This acyl-Coenzyme A dehydrogenase is specific to long-chain and very-long-chain fatty acids. A deficiency in this gene product reduces myocardial fatty acid beta-oxidation and is associated with cardiomyopathy. Alternative splicing results in multiple transcript variants encoding different isoforms.

Gene names and symbols associated with ACADVL

  • acyl-CoA dehydrogenase, very long chain (ACADVL) antibody
  • acyl-CoA dehydrogenase, very long chain (Acadvl) antibody
  • acyl-Coenzyme A dehydrogenase, very long chain (acadvl) antibody
  • acyl-Coenzyme A dehydrogenase, very long chain (Acadvl) antibody
  • ACAD6 antibody
  • fb52d04 antibody
  • LCACD antibody
  • vlcad antibody
  • wu:fb52d04 antibody
  • wu:fc75e01 antibody
  • zgc:64067 antibody

Protein level used designations for ACADVL

acyl-Coenzyme A dehydrogenase, very long chain , very long-chain specific acyl-CoA dehydrogenase, mitochondrial , VLCAD , acyl-coenzyme A dehydrogenase, very long chain , VLCAD very-long-chain acyl-CoA dehydrogenase , Very long chain Acyl-Coa dehydrogenase , vlcad , MVLCAD

GENE ID SPECIES
100061583 Equus caballus
37 Homo sapiens
489463 Canis lupus familiaris
282130 Bos taurus
25363 Rattus norvegicus
573723 Danio rerio
11370 Mus musculus
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