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Glycine Cleavage System H Protein Proteins (GCSH)

Degradation of glycine is brought about by the glycine cleavage system, which is composed of four mitochondrial protein components: P protein (a pyridoxal phosphate-dependent glycine decarboxylase), H protein (a lipoic acid-containing protein), T protein (a tetrahydrofolate-requiring enzyme), and L protein (a lipoamide dehydrogenase). Additionally we are shipping Glycine Cleavage System H Protein Antibodies (54) and Glycine Cleavage System H Protein Kits (5) and many more products for this protein.

list all proteins Gene Name GeneID UniProt
GCSH 2653 P23434
GCSH 68133 Q91WK5
GCSH 171133 Q5I0P2
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Top Glycine Cleavage System H Protein Proteins at antibodies-online.com

Showing 10 out of 10 products:

Catalog No. Origin Source Conjugate Images Quantity Supplier Delivery Price Details
HOST_Escherichia coli (E. coli) Human His tag „Crystallography Grade“ protein due to multi-step, protein-specific purification process 1 mg Log in to see 29 to 34 Days
$4,331.68
Details
HOST_Escherichia coli (E. coli) Mouse His tag „Crystallography Grade“ protein due to multi-step, protein-specific purification process 1 mg Log in to see 29 to 34 Days
$4,331.68
Details
HOST_Escherichia coli (E. coli) Human His tag 100 μg Log in to see 7 to 8 Days
$319.00
Details
HOST_Escherichia coli (E. coli) Human His tag 100 μg Log in to see 16 Days
$437.80
Details
HOST_Wheat germ Human GST tag 10 μg Log in to see 9 Days
$405.71
Details
Yeast Cow His tag   1 mg Log in to see 56 to 66 Days
$2,253.17
Details
Yeast Rat His tag   1 mg Log in to see 56 to 66 Days
$2,253.17
Details
Yeast Chicken His tag   1 mg Log in to see 56 to 66 Days
$2,253.17
Details
Yeast Rabbit His tag   1 mg Log in to see 56 to 66 Days
$2,253.17
Details
HOST_Human Human Un-conjugated   20 μg Log in to see 9 to 11 Days
$785.40
Details

GCSH Proteins by Origin and Source

Origin Expressed in Conjugate
Human , ,
,
Mouse (Murine)

Rat (Rattus)

Top referenced Glycine Cleavage System H Protein Proteins

  1. Human GCSH Protein expressed in Escherichia coli (E. coli) - ABIN667601 : Koyata, Hiraga: The glycine cleavage system: structure of a cDNA encoding human H-protein, and partial characterization of its gene in patients with hyperglycinemias. in American journal of human genetics 1991 (PubMed)
    Show all 2 references for ABIN667601

More Proteins for Glycine Cleavage System H Protein (GCSH) Interaction Partners

Cow (Bovine) Glycine Cleavage System H Protein (GCSH) interaction partners

  1. X-ray crystal structure of bovine H-protein (show MYBPH Proteins), a component of the glycine cleavage system, was determined at 0.88 A resolution.

Human Glycine Cleavage System H Protein (GCSH) interaction partners

  1. Data indicate no mutation was found in glycine cleavage system protein-H (GCSH) and suggest that mutations in both glycine decarboxylase (GLDC (show GLDC Proteins)) and aminomethyltransferase (AMT (show AMT Proteins)) are the main cause of glycine encephalopathy in Malaysian population.

  2. Heterozygous GCSH gene mutation in transient neonatal hyperglycinemia.

  3. Genetic analysis showed a non-previously described mutation affecting a consensus splice site (IVS2-1G > C 3) in the AMT (show AMT Proteins) gene encoding the T protein of the glycine cleavage system.

Glycine Cleavage System H Protein (GCSH) Protein Profile

Protein Summary

Degradation of glycine is brought about by the glycine cleavage system, which is composed of four mitochondrial protein components: P protein (a pyridoxal phosphate-dependent glycine decarboxylase), H protein (a lipoic acid-containing protein), T protein (a tetrahydrofolate-requiring enzyme), and L protein (a lipoamide dehydrogenase). The protein encoded by this gene is the H protein, which transfers the methylamine group of glycine from the P protein to the T protein. Defects in this gene are a cause of nonketotic hyperglycinemia (NKH). Two transcript variants, one protein-coding and the other probably not protein-coding,have been found for this gene. Also, several transcribed and non-transcribed pseudogenes of this gene exist throughout the genome.

Gene names and symbols associated with GCSH

  • glycine cleavage system protein H (aminomethyl carrier) (GCSH)
  • glycine cleavage system H protein (gcvH-2)
  • glycine cleavage system H protein (gcvH-1)
  • glycine cleavage system H protein (gcvH)
  • glycine cleavage system protein H (aminomethyl carrier), a (gcsha)
  • glycine cleavage system protein H (gcvH)
  • glycine cleavage system protein H (gcvH-2)
  • glycine cleavage system protein H (aminomethyl carrier) (Gcsh)
  • leucine rich repeat containing 34 (LRRC34)
  • 1100001L02Rik protein
  • 5730591C18Rik protein
  • BA5228 protein
  • GCE protein
  • GCSH protein
  • H-PROTEIN protein
  • NKH protein
  • wu:fb14d10 protein
  • wu:fw84b08 protein
  • zgc:112535 protein

Protein level used designations for GCSH

glycine cleavage system protein H (aminomethyl carrier) , glycine cleavage system H protein , glycine cleavage system protein H , glycine cleavage system H protein, mitochondrial , lipoic acid-containing protein , mitochondrial glycine cleavage system H-protein , hydrogen carrier protein , H protein

GENE ID SPECIES
468042 Pan troglodytes
479633 Canis lupus familiaris
508238 Bos taurus
742399 Pan troglodytes
100138886 Bos taurus
2688047 Geobacter sulfurreducens PCA
3195867 Ruegeria pomeroyi DSS-3
3727553 Carboxydothermus hydrogenoformans Z-2901
541329 Danio rerio
1084664 Bacillus anthracis str. Ames
1168635 Shewanella oneidensis MR-1
1209626 Coxiella burnetii RSA 493
2799475 Listeria monocytogenes serotype 4b str. F2365
3196781 Ruegeria pomeroyi DSS-3
2653 Homo sapiens
68133 Mus musculus
171133 Rattus norvegicus
317723 Bos taurus
415803 Gallus gallus
100009476 Oryctolagus cuniculus
512714 Bos taurus
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