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anti-Hydroxyacyl-CoA Dehydrogenase/3-Ketoacyl-CoA Thiolase/enoyl-CoA Hydratase (Trifunctional Protein), beta Subunit (HADHB) Antibodies

HADHB encodes the beta subunit of the mitochondrial trifunctional protein, which catalyzes the last three steps of mitochondrial beta-oxidation of long chain fatty acids. Additionally we are shipping Hydroxyacyl-CoA Dehydrogenase/3-Ketoacyl-CoA Thiolase/enoyl-CoA Hydratase (Trifunctional Protein), beta Subunit Proteins (9) and Hydroxyacyl-CoA Dehydrogenase/3-Ketoacyl-CoA Thiolase/enoyl-CoA Hydratase (Trifunctional Protein), beta Subunit Kits (5) and many more products for this protein.

list all antibodies Gene Name GeneID UniProt
HADHB 3032 P55084
HADHB 171155 Q60587
HADHB 231086 Q99JY0
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Top anti-Hydroxyacyl-CoA Dehydrogenase/3-Ketoacyl-CoA Thiolase/enoyl-CoA Hydratase (Trifunctional Protein), beta Subunit Antibodies at antibodies-online.com

Showing 10 out of 76 products:

Catalog No. Reactivity Host Conjugate Application Images Quantity Supplier Delivery Price Details
Chicken Rabbit Un-conjugated IHC, WB 100 μL Log in to see 2 to 3 Days
$289.00
Details
Human Rabbit Un-conjugated EIA, FACS, WB Flow cytometric analysis of Jurkat cells using HADHB Antibody (C-term) Cat.-No AP51996PU-N (right histogram) compared to a negative control cell (left histogram). FITC-conjugated goat-anti-rabbit secondary antibodies were used for the analysis. Western blot analysis of HADHB Antibody (C-term) in Jurkat cell line lysates (35ug/lane). HADHB (arrow) was detected using the purified Pab. 0.4 mL Log in to see 6 to 8 Days
$390.50
Details
Human Rabbit Un-conjugated FACS, WB Western blot analysis of HADHB Antibody (C-term) (ABIN653816) in Jurkat cell line lysates (35 µg/lane). HADHB (arrow) was detected using the purified polyclonal antibody. HADHB Antibody (C-term) (ABIN653816) flow cytometric analysis of Jurkat cells (right histogram) compared to a negative control cell (left histogram).FITC-conjugated goat-anti-rabbit secondary antibodies were used for the analysis. 400 μL Log in to see 10 to 11 Days
$324.50
Details
Human Rabbit Un-conjugated WB WB Image Sample (30 ug of whole cell lysate) A: A431 , 10% SDS PAGE HADHB antibody antibody diluted at 1:1000 100 μL Log in to see 2 to 3 Days
$358.60
Details
Human Rabbit Un-conjugated IHC (p), WB Human Pancreas: Formalin-Fixed, Paraffin-Embedded (FFPE) Human Adrenal: Formalin-Fixed, Paraffin-Embedded (FFPE) 50 μg Log in to see 8 to 10 Days
$676.50
Details
Human Rabbit Un-conjugated IHC, ELISA, WB 50 μg Log in to see 2 to 3 Days
$433.13
Details
Human Rabbit Un-conjugated WB   100 μL Log in to see 8 to 10 Days
$507.83
Details
Human Rabbit Un-conjugated IHC, WB HADHB antibody was used for immunohistochemistry at a concentration of 4-8 ug/ml. Magnification is at 400X HADHB antibody was used for immunohistochemistry at a concentration of 4-8 ug/ml. Magnification is at 400X 50 μg Log in to see 3 to 4 Days
$473.93
Details
Human Rabbit Un-conjugated WB 100 μL Log in to see 6 to 11 Days
$485.71
Details
Human Rabbit Un-conjugated WB   50 μL Log in to see 8 to 10 Days
$390.50
Details

HADHB Antibodies by Reactivity, Application, Clonality and Conjugate

Attributes Applications Host Clonality Conjugate
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Top referenced anti-Hydroxyacyl-CoA Dehydrogenase/3-Ketoacyl-CoA Thiolase/enoyl-CoA Hydratase (Trifunctional Protein), beta Subunit Antibodies

  1. Human Polyclonal HADHB Primary Antibody for EIA, FACS - ABIN952676 : Purevsuren, Fukao, Hasegawa, Kobayashi, Li, Mushimoto, Fukuda, Yamaguchi: Clinical and molecular aspects of Japanese patients with mitochondrial trifunctional protein deficiency. in Molecular genetics and metabolism 2009 (PubMed)
    Show all 3 references for ABIN952676

  2. Chicken Polyclonal HADHB Primary Antibody for IHC, WB - ABIN2783232 : Wang, Yang, Zhu, Wang, Yang, Wang, Zhai, Li, Yu: [Screening for G1528C mutation in mitochondrial trifunctional protein gene in pregnant women with severe preeclampsia and new born infant]. in Zhonghua fu chan ke za zhi 2007 (PubMed)
    Show all 2 references for ABIN2783232

More Antibodies against Hydroxyacyl-CoA Dehydrogenase/3-Ketoacyl-CoA Thiolase/enoyl-CoA Hydratase (Trifunctional Protein), beta Subunit Interaction Partners

Human Hydroxyacyl-CoA Dehydrogenase/3-Ketoacyl-CoA Thiolase/enoyl-CoA Hydratase (Trifunctional Protein), beta Subunit (HADHB) interaction partners

  1. Exposure to bezafibrate (400 muM for 48 h) increased the abundance of HADHA (show HADHA Antibodies) and HADHB mRNAs.

  2. nonstructural protein 5 (show CAPS Antibodies) (NS5 (show RAF1 Antibodies)) interacted with hydroxyacyl-CoA dehydrogenase (show HADH Antibodies) alpha and beta subunits, two components of the mitochondrial trifunctional protein (MTP) involved in LCFA beta-oxidation

  3. Mutations in HADHB, which encodes the beta-subunit of mitochondrial trifunctional protein, cause infantile onset hypoparathyroidism and peripheral polyneuropathy.

  4. Heterozygous mutation in HADHB gene cause early-onset axonal axonal Charcot-Marie-tooth disease.

  5. The results demonstrated that ERbeta (show ESR2 Antibodies) was indeed associated and colocalized with HADHB within mitochondria.

  6. HADHB is a functional molecular target of estrogen receptor alpha (show ESR1 Antibodies) in the mitochondria, and the interaction may play an important role in the estrogen-mediated lipid metabolism in animals and humans.

  7. mutational analysis of the HADHB gene, which encodes long-chain 3-ketoacyl-CoA thiolase, identified compound heterozygous mutations of c.520C>T (p.R141C) and c.1331G>A (p.R411K) in a case of mitochondrial trifunctional protein deficiency

  8. Results emphasize the value of cDNA analysis in the characterization of HADHA (show HADHA Antibodies) and HADHB mutations and further strengthen the model of haploinsufficiency as a major pathomechanism in MTP defects.

  9. Recombinant mitochondrial trifunctional protein displayed 2-enoyl-CoA hydratase, l-3-hydroxyacyl-CoA dehydrogenase, and 3-ketoacyl-CoA thiolase activities.

  10. The present findings showed that all missense mutations in HADHB were disease-causing.

Cow (Bovine) Hydroxyacyl-CoA Dehydrogenase/3-Ketoacyl-CoA Thiolase/enoyl-CoA Hydratase (Trifunctional Protein), beta Subunit (HADHB) interaction partners

  1. Mutation analysis of the HADHB gene of patient 4 identified compound heterozygosity of N114D/N307D.

Mouse (Murine) Hydroxyacyl-CoA Dehydrogenase/3-Ketoacyl-CoA Thiolase/enoyl-CoA Hydratase (Trifunctional Protein), beta Subunit (HADHB) interaction partners

  1. nonstructural protein 5 (show CAPS Antibodies) (NS5 (show RAF1 Antibodies)) interacted with hydroxyacyl-CoA dehydrogenase (show HADH Antibodies) alpha and beta subunits, two components of the mitochondrial trifunctional protein (MTP (show LAPTM4A Antibodies)) involved in LCFA beta-oxidation

Hydroxyacyl-CoA Dehydrogenase/3-Ketoacyl-CoA Thiolase/enoyl-CoA Hydratase (Trifunctional Protein), beta Subunit (HADHB) Antigen Profile

Protein Summary

This gene encodes the beta subunit of the mitochondrial trifunctional protein, which catalyzes the last three steps of mitochondrial beta-oxidation of long chain fatty acids. The mitochondrial membrane-bound heterocomplex is composed of four alpha and four beta subunits, with the beta subunit catalyzing the 3-ketoacyl-CoA thiolase activity. Mutations in this gene result in trifunctional protein deficiency. The encoded protein can also bind RNA and decreases the stability of some mRNAs. The genes of the alpha and beta subunits of the mitochondrial trifunctional protein are located adjacent to each other in the human genome in a head-to-head orientation. Alternatively spliced transcript variants have been found\; however, their full-length nature is not known.

Gene names and symbols associated with HADHB

  • hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), beta subunit (HADHB) antibody
  • hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), beta subunit (hadhb) antibody
  • hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), beta subunit (Hadhb) antibody
  • hydroxyacyl-Coenzyme A dehydrogenase/3-ketoacyl-Coenzyme A thiolase/enoyl-Coenzyme A hydratase (trifunctional protein), beta subunit (hadhb) antibody
  • hydroxyacyl-Coenzyme A dehydrogenase/3-ketoacyl-Coenzyme A thiolase/enoyl-Coenzyme A hydratase (trifunctional protein), beta subunit (Hadhb) antibody
  • long-chain 3-ketoacyl-CoA thiolase (LCTHIO) antibody
  • 4930479F15Rik antibody
  • ECHB antibody
  • fb14g10 antibody
  • Hadhb antibody
  • Mtpb antibody
  • thiolase antibody
  • TP-BETA antibody
  • wu:fb14g10 antibody
  • zgc:56274 antibody

Protein level used designations for HADHB

2-enoyl-Coenzyme A (CoA) hydratase, beta subunit , 3-ketoacyl-Coenzyme A (CoA) thiolase of mitochondrial trifunctional protein, beta subunit , acetyl-CoA acyltransferase , beta-ketothiolase , hydroxyacyl-Coenzyme A dehydrogenase/3-ketoacyl-Coenzyme A thiolase/enoyl-Coenzyme A hydratase (trifunctional protein), beta subunit , trifunctional enzyme subunit beta, mitochondrial , hydroxyacyl dehydrogenase, subunit B , TP-beta , dehydrogenase/3-ketoacyl-Coenzyme A thiolase/enoyl-Coenzyme A hydratase (trifunctional protein), beta subunit , mitochondrial trifunctional protein, beta subunit , 3-ketoacyl-Coenzyme A thiolase , TP-Beta , enoyl-Coenzyme A hydratase, beta subunit , trifunctional enzyme beta subunit, mitochondrial , dehydrogenase/3-ketoacyl-Coenzyme A thiolase , hydroxyacyl-Coenzyme A dehydrogenase/3-ketoacyl-Coenzyme A thiolase/enoyl-Coenzyme A hydratase (trifunctional protein), beta aubunit

GENE ID SPECIES
3032 Homo sapiens
379769 Xenopus laevis
421995 Gallus gallus
281811 Bos taurus
171155 Rattus norvegicus
607926 Canis lupus familiaris
459080 Pan troglodytes
336606 Danio rerio
231086 Mus musculus
397017 Sus scrofa
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