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Hydroxyacyl-CoA Dehydrogenase/3-Ketoacyl-CoA Thiolase/enoyl-CoA Hydratase (Trifunctional Protein), beta Subunit (HADHB) ELISA Kits

HADHB encodes the beta subunit of the mitochondrial trifunctional protein, which catalyzes the last three steps of mitochondrial beta-oxidation of long chain fatty acids. Additionally we are shipping Hydroxyacyl-CoA Dehydrogenase/3-Ketoacyl-CoA Thiolase/enoyl-CoA Hydratase (Trifunctional Protein), beta Subunit Antibodies (77) and Hydroxyacyl-CoA Dehydrogenase/3-Ketoacyl-CoA Thiolase/enoyl-CoA Hydratase (Trifunctional Protein), beta Subunit Proteins (9) and many more products for this protein.

list all ELISA KIts Gene Name GeneID UniProt
HADHB 3032 P55084
HADHB 171155 Q60587
HADHB 231086 Q99JY0
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Top Hydroxyacyl-CoA Dehydrogenase/3-Ketoacyl-CoA Thiolase/enoyl-CoA Hydratase (Trifunctional Protein), beta Subunit ELISA Kits at antibodies-online.com

Showing 3 out of 5 products:

Catalog No. Reactivity Sensitivity Range Images Quantity Supplier Delivery Price Details
Mouse 0.59 ng/mL 1.56-100 ng/mL 96 Tests Log in to see 9 to 11 Days
$757.89
Details
Rat 0.129 ng/mL 0.31-20 ng/mL 96 Tests Log in to see 9 to 11 Days
$800.00
Details
Human 6.25 pg/ml 25-1600 pg/mL   96 Tests Log in to see 9 to 11 Days
$1,026.67
Details

More ELISA Kits for Hydroxyacyl-CoA Dehydrogenase/3-Ketoacyl-CoA Thiolase/enoyl-CoA Hydratase (Trifunctional Protein), beta Subunit Interaction Partners

Human Hydroxyacyl-CoA Dehydrogenase/3-Ketoacyl-CoA Thiolase/enoyl-CoA Hydratase (Trifunctional Protein), beta Subunit (HADHB) interaction partners

  1. Exposure to bezafibrate (400 muM for 48 h) increased the abundance of HADHA (show HADHA ELISA Kits) and HADHB mRNAs.

  2. nonstructural protein 5 (show CAPS ELISA Kits) (NS5 (show RAF1 ELISA Kits)) interacted with hydroxyacyl-CoA dehydrogenase (show HADH ELISA Kits) alpha and beta subunits, two components of the mitochondrial trifunctional protein (MTP) involved in LCFA beta-oxidation

  3. Mutations in HADHB, which encodes the beta-subunit of mitochondrial trifunctional protein, cause infantile onset hypoparathyroidism and peripheral polyneuropathy.

  4. Heterozygous mutation in HADHB gene cause early-onset axonal axonal Charcot-Marie-tooth disease.

  5. The results demonstrated that ERbeta (show ESR2 ELISA Kits) was indeed associated and colocalized with HADHB within mitochondria.

  6. HADHB is a functional molecular target of estrogen receptor alpha (show ESR1 ELISA Kits) in the mitochondria, and the interaction may play an important role in the estrogen-mediated lipid metabolism in animals and humans.

  7. mutational analysis of the HADHB gene, which encodes long-chain 3-ketoacyl-CoA thiolase, identified compound heterozygous mutations of c.520C>T (p.R141C) and c.1331G>A (p.R411K) in a case of mitochondrial trifunctional protein deficiency

  8. Results emphasize the value of cDNA analysis in the characterization of HADHA (show HADHA ELISA Kits) and HADHB mutations and further strengthen the model of haploinsufficiency as a major pathomechanism in MTP defects.

  9. Recombinant mitochondrial trifunctional protein displayed 2-enoyl-CoA hydratase, l-3-hydroxyacyl-CoA dehydrogenase, and 3-ketoacyl-CoA thiolase activities.

  10. The present findings showed that all missense mutations in HADHB were disease-causing.

Cow (Bovine) Hydroxyacyl-CoA Dehydrogenase/3-Ketoacyl-CoA Thiolase/enoyl-CoA Hydratase (Trifunctional Protein), beta Subunit (HADHB) interaction partners

  1. Mutation analysis of the HADHB gene of patient 4 identified compound heterozygosity of N114D/N307D.

Mouse (Murine) Hydroxyacyl-CoA Dehydrogenase/3-Ketoacyl-CoA Thiolase/enoyl-CoA Hydratase (Trifunctional Protein), beta Subunit (HADHB) interaction partners

  1. nonstructural protein 5 (show CAPS ELISA Kits) (NS5 (show RAF1 ELISA Kits)) interacted with hydroxyacyl-CoA dehydrogenase (show HADH ELISA Kits) alpha and beta subunits, two components of the mitochondrial trifunctional protein (MTP (show LAPTM4A ELISA Kits)) involved in LCFA beta-oxidation

Hydroxyacyl-CoA Dehydrogenase/3-Ketoacyl-CoA Thiolase/enoyl-CoA Hydratase (Trifunctional Protein), beta Subunit (HADHB) Antigen Profile

Antigen Summary

This gene encodes the beta subunit of the mitochondrial trifunctional protein, which catalyzes the last three steps of mitochondrial beta-oxidation of long chain fatty acids. The mitochondrial membrane-bound heterocomplex is composed of four alpha and four beta subunits, with the beta subunit catalyzing the 3-ketoacyl-CoA thiolase activity. Mutations in this gene result in trifunctional protein deficiency. The encoded protein can also bind RNA and decreases the stability of some mRNAs. The genes of the alpha and beta subunits of the mitochondrial trifunctional protein are located adjacent to each other in the human genome in a head-to-head orientation. Alternatively spliced transcript variants have been found\; however, their full-length nature is not known.

Gene names and symbols associated with HADHB

  • hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), beta subunit (HADHB) antibody
  • hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), beta subunit (hadhb) antibody
  • hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), beta subunit (Hadhb) antibody
  • hydroxyacyl-Coenzyme A dehydrogenase/3-ketoacyl-Coenzyme A thiolase/enoyl-Coenzyme A hydratase (trifunctional protein), beta subunit (hadhb) antibody
  • hydroxyacyl-Coenzyme A dehydrogenase/3-ketoacyl-Coenzyme A thiolase/enoyl-Coenzyme A hydratase (trifunctional protein), beta subunit (Hadhb) antibody
  • long-chain 3-ketoacyl-CoA thiolase (LCTHIO) antibody
  • 4930479F15Rik antibody
  • ECHB antibody
  • fb14g10 antibody
  • Hadhb antibody
  • Mtpb antibody
  • thiolase antibody
  • TP-BETA antibody
  • wu:fb14g10 antibody
  • zgc:56274 antibody

Protein level used designations for HADHB

2-enoyl-Coenzyme A (CoA) hydratase, beta subunit , 3-ketoacyl-Coenzyme A (CoA) thiolase of mitochondrial trifunctional protein, beta subunit , acetyl-CoA acyltransferase , beta-ketothiolase , hydroxyacyl-Coenzyme A dehydrogenase/3-ketoacyl-Coenzyme A thiolase/enoyl-Coenzyme A hydratase (trifunctional protein), beta subunit , trifunctional enzyme subunit beta, mitochondrial , hydroxyacyl dehydrogenase, subunit B , TP-beta , dehydrogenase/3-ketoacyl-Coenzyme A thiolase/enoyl-Coenzyme A hydratase (trifunctional protein), beta subunit , mitochondrial trifunctional protein, beta subunit , 3-ketoacyl-Coenzyme A thiolase , TP-Beta , enoyl-Coenzyme A hydratase, beta subunit , trifunctional enzyme beta subunit, mitochondrial , dehydrogenase/3-ketoacyl-Coenzyme A thiolase , hydroxyacyl-Coenzyme A dehydrogenase/3-ketoacyl-Coenzyme A thiolase/enoyl-Coenzyme A hydratase (trifunctional protein), beta aubunit

GENE ID SPECIES
3032 Homo sapiens
379769 Xenopus laevis
421995 Gallus gallus
281811 Bos taurus
171155 Rattus norvegicus
607926 Canis lupus familiaris
459080 Pan troglodytes
336606 Danio rerio
231086 Mus musculus
397017 Sus scrofa
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