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anti-Methylcrotonoyl-CoA Carboxylase 1 (Alpha) (MCCC1) Antibodies

MCCC1 encodes the large subunit of 3-methylcrotonyl-CoA carboxylase. Additionally we are shipping Methylcrotonoyl-CoA Carboxylase 1 (Alpha) Proteins (5) and Methylcrotonoyl-CoA Carboxylase 1 (Alpha) Kits (1) and many more products for this protein.

list all antibodies Gene Name GeneID UniProt
MCCC1 56922 Q96RQ3
MCCC1 294972 Q5I0C3
MCCC1 72039 Q99MR8
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Top anti-Methylcrotonoyl-CoA Carboxylase 1 (Alpha) Antibodies at antibodies-online.com

Showing 10 out of 31 products:

Catalog No. Reactivity Host Conjugate Application Images Quantity Supplier Delivery Price Details
Human Mouse Un-conjugated ELISA, WB Detection limit for recombinant GST tagged MCCC1 is approximately 0.1 ng/mL as a capture antibody. 0.1 mg Log in to see 8 to 11 Days
$450.00
Details
Human Rabbit Un-conjugated WB MCCC1 Antibody (Center) (ABIN651863) western blot analysis in mouse liver tissue lysates (15 µg/lane). This demonstrates the MCCC1 antibody detected MCCC1 protein (arrow). 400 μL Log in to see 10 to 11 Days
$324.50
Details
Human Rabbit APC ELISA, WB   200 μL Log in to see 8 to 10 Days
$969.83
Details
Human Mouse Un-conjugated ELISA, WB Detection limit for recombinant GST tagged MCCC1 is approximately 0.1ng/ml as a capture antibody. Western Blot detection against Immunogen (36.74 KDa) . 100 μg Log in to see 9 Days
$430.00
Details
Human Rabbit Un-conjugated ELISA   200 μL Log in to see 8 to 10 Days
$713.17
Details
Human Rabbit HRP ELISA, WB   200 μL Log in to see 8 to 10 Days
$969.83
Details
Human Mouse Un-conjugated WB Western Blot analysis of MCCC1 expression in transfected 293T cell line by MCCC1 MaxPab polyclonal antibody.Lane 1: MCCC1 transfected lysate(79.75 KDa).Lane 2: Non-transfected lysate. 50 μg Log in to see 9 Days
$430.00
Details
Human Rabbit Un-conjugated ELISA, WB   200 μL Log in to see 11 to 16 Days
$532.71
Details
Human Rabbit APC ELISA, WB   200 μL Log in to see 16 Days
$710.29
Details
Human Rabbit FITC ELISA, WB   200 μL Log in to see 16 Days
$710.29
Details

MCCC1 Antibodies by Reactivity, Application, Clonality and Conjugate

Attributes Applications Host Clonality Conjugate
Human ,
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,
, , , , ,
Rat (Rattus)


Mouse (Murine)


Top referenced anti-Methylcrotonoyl-CoA Carboxylase 1 (Alpha) Antibodies

  1. Human Monoclonal MCCC1 Primary Antibody for ELISA, WB - ABIN395693 : Rose, Behm, Drgon, Johnson, Uhl: Personalized smoking cessation: interactions between nicotine dose, dependence and quit-success genotype score. in Molecular medicine (Cambridge, Mass.) 2010 (PubMed)
    Show all 5 references for ABIN395693

More Antibodies against Methylcrotonoyl-CoA Carboxylase 1 (Alpha) Interaction Partners

Human Methylcrotonoyl-CoA Carboxylase 1 (Alpha) (MCCC1) interaction partners

  1. Novel mutations in MCCC1 gene were identified in Chinese population. The expression profiles of two splice mutations (c.639+2T>A and c.639+5G>T) were also characterized.

  2. Four new point mutations were detected in the MCCC1 gene in patients with maternal 3-methylcrotonyl coenzyme deficiency.

  3. This study demonistrated that Mainland China demonstrates that MCCC1/LAMP3 (show CD63 Antibodies) (rs11711441) is associated with a lower risk of Parkinson's disease.

  4. 3-methylcrotonyl-CoA carboxylase (show MCCC2 Antibodies) inhibition has a role in increased excretion of 3-hydroxyisovaleric acid in valproate-treated patients

  5. Mutation in 3-methylcrotonyl CoA carboxylase 1 gene is associated with 3-methylcrotonyl-CoA carboxylase (show MCCC2 Antibodies) deficiency.

  6. study reports eight different mutant alleles of MCCC1 or MCCC2 (show MCCC2 Antibodies) including six novel mutations in Korean patients with 3-methylcrotonyl-CoA carboxylase (show MCCC2 Antibodies) (MCC (show MCC Antibodies)) deficiency

  7. identified two novel MCCA and four novel MCCB mutant alleles from five MCC (show MCC Antibodies)-deficient patients

  8. factors other than the genotype at the MCCA and MCCB loci have a major influence on the phenotype of MCC (show MCC Antibodies) deficiency

  9. The amino-termini containing 39 (MCCalpha) or 20 amino acids (MCCbeta) were both necessary and sufficient for targeting. Structural requirements for mitochondrial import were defined by site-directed mutagenesis.

  10. Molecular analyses revealed novel mutations in one of the causative genes, MCCA or MCCB, in all five of the MCC (show MCC Antibodies) deficiency patients

Arabidopsis thaliana Methylcrotonoyl-CoA Carboxylase 1 (Alpha) (MCCC1) interaction partners

  1. Studies indicate that mutations in either 3-methylcrotonyl CoA carboxylase (show MCCC2 Antibodies) MCCA (At1g03090) or MCCB (show MCCC2 Antibodies) (At4g34030) block mitochondrial Leu catabolism, as inferred from the increased accumulation of Leu.

Methylcrotonoyl-CoA Carboxylase 1 (Alpha) (MCCC1) Antigen Profile

Protein Summary

This gene encodes the large subunit of 3-methylcrotonyl-CoA carboxylase. This enzyme functions as a heterodimer and catalyzes the carboxylation of 3-methylcrotonyl-CoA to form 3-methylglutaconyl-CoA. Mutations in this gene are associated with 3-Methylcrotonylglycinuria, an autosomal recessive disorder of leucine catabolism.

Gene names and symbols associated with MCCC1

  • methylcrotonoyl-CoA carboxylase 1 (alpha) (MCCC1) antibody
  • methylcrotonoyl-CoA carboxylase 1 (alpha) (Mccc1) antibody
  • methylcrotonoyl-CoA carboxylase subunit alpha (MCCA) antibody
  • methylcrotonoyl-Coenzyme A carboxylase 1 (alpha) (Mccc1) antibody
  • 1810045E08Rik antibody
  • 2310058B18Rik antibody
  • MCC-B antibody
  • Mcca antibody
  • MCCalpha antibody
  • R75106 antibody

Protein level used designations for MCCC1

3-methylcrotonyl-CoA carboxylase 1 , 3-methylcrotonyl-CoA carboxylase biotin-containing subunit , 3-methylcrotonyl-CoA:carbon dioxide ligase subunit alpha , MCCase subunit alpha , methylcrotonoyl-CoA carboxylase subunit alpha, mitochondrial , methylcrotonoyl-Coenzyme A carboxylase 1 (alpha)

GENE ID SPECIES
56922 Homo sapiens
294972 Rattus norvegicus
838362 Arabidopsis thaliana
72039 Mus musculus
Selected quality suppliers for anti-Methylcrotonoyl-CoA Carboxylase 1 (Alpha) (MCCC1) Antibodies
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