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anti-Methylcrotonoyl-CoA Carboxylase 2 (Beta) (MCCC2) Antibodies

MCCC2 encodes the small subunit of 3-methylcrotonyl-CoA carboxylase. Additionally we are shipping Methylcrotonoyl-CoA Carboxylase 2 (Beta) Proteins (5) and Methylcrotonoyl-CoA Carboxylase 2 (Beta) Kits (1) and many more products for this protein.

list all antibodies Gene Name GeneID UniProt
MCCC2 64087 Q9HCC0
MCCC2 361884 Q5XIT9
MCCC2 78038 Q3ULD5
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Top anti-Methylcrotonoyl-CoA Carboxylase 2 (Beta) Antibodies at antibodies-online.com

Showing 10 out of 61 products:

Catalog No. Reactivity Host Conjugate Application Images Quantity Supplier Delivery Price Details
Human Rabbit Un-conjugated EIA, WB (LEFT) Western blot analysis of MCCC2 Antibody (Center) in CEM, 293 cell line lysates (35ug/lane). MCCC2 (arrow) was detected using the purified Pab. (RIGHT) Western blot analysis of MCCC2 Antibody (Center) in mouse liver tissue lysates (35ug/lane). MCCC2 (arrow) was detected using the purified Pab. 0.4 mL Log in to see 6 to 8 Days
$390.50
Details
Human Mouse Un-conjugated ELISA, WB MCCC2 polyclonal antibody (A01), Lot # 051212JC01 Western Blot analysis of MCCC2 expression in MES-SA/Dx5 . Western Blot detection against Immunogen (37.99 KDa) . 50 μL Log in to see 9 Days
$298.57
Details
Human Rabbit Un-conjugated IHC (p), WB IHC-P Image MCCC2 antibody [N1C1] detects MCCC2 protein at mitochondria in mouse cervix by immunohistochemical analysis. Sample: Paraffin-embedded mouse cervix. MCCC2 antibody [N1C1] , diluted at 1:500. WB Image Sample (50 ug of whole cell lysate) A: mouse liver 7.5% SDS PAGE antibody diluted at 1:1000 100 μL Log in to see 2 to 3 Days
$358.60
Details
Human Rabbit Un-conjugated WB MCCC2 Antibody (C-term)  western blot analysis in NCI-H292 cell line lysates (35ug/lane).This demonstrates the MCCC2 antibody detected the MCCC2 protein (arrow). 400 μL Log in to see 10 to 11 Days
$324.50
Details
Human Rabbit Un-conjugated FACS, IHC (p), WB Western blot analysis of MCCC2 Antibody (Center) (ABIN390911) in CEM, 293 cell line lysates (35 µg/lane). MCCC2 (arrow) was detected using the purified polyclonal antibody. Western blot analysis of MCCC2 Antibody (Center) (ABIN390911) in mouse liver tissue lysates (35 µg/lane). MCCC2 (arrow) was detected using the purified polyclonal antibody. 400 μL Log in to see 10 to 11 Days
$324.50
Details
Human Mouse Un-conjugated IF, WB Western Blot analysis of MCCC2 expression in transfected 293T cell line by MCCC2 MaxPab polyclonal antibody.Lane 1: MCCC2 transfected lysate(61.93 KDa).Lane 2: Non-transfected lysate. MCCC2 MaxPab polyclonal antibody. Western Blot analysis of MCCC2 expression in human liver. 50 μg Log in to see 9 Days
$430.00
Details
Human Rabbit Alkaline Phosphatase (AP) ELISA, WB   200 μL Log in to see 8 to 10 Days
$969.83
Details
Human Rabbit Un-conjugated WB 100 μL Log in to see 2 to 3 Days
$289.00
Details
Human Mouse Un-conjugated IHC (p), ELISA, WB Immunoperoxidase of monoclonal antibody to MCCC2 on formalin-fixed paraffin-embedded human liver. [antibody concentration 3 ug/ml] Detection limit for recombinant GST tagged MCCC2 is 0.1 ng/ml as a capture antibody. 100 μg Log in to see 9 Days
$430.00
Details
Human Rabbit Un-conjugated WB 400 μL Log in to see 6 Days
$457.14
Details

MCCC2 Antibodies by Reactivity, Application, Clonality and Conjugate

Attributes Applications Host Clonality Conjugate
Human ,
,
,
, , , , ,
Rat (Rattus)


Mouse (Murine)


Top referenced anti-Methylcrotonoyl-CoA Carboxylase 2 (Beta) Antibodies

  1. Human Polyclonal MCCC2 Primary Antibody for IF, WB - ABIN528514 : Grünert, Stucki, Morscher, Suormala, Bürer, Burda, Christensen, Ficicioglu, Herwig, Kölker, Möslinger, Pasquini, Santer, Schwab, Wilcken, Fowler, Yue, Baumgartner: 3-methylcrotonyl-CoA carboxylase deficiency: clinical, biochemical, enzymatic and molecular studies in 88 individuals. in Orphanet journal of rare diseases 2012 (PubMed)

  2. Human Polyclonal MCCC2 Primary Antibody for ELISA, WB - ABIN566228 : Stucki, Suormala, Fowler, Valle, Baumgartner: Cryptic exon activation by disruption of exon splice enhancer: novel mechanism causing 3-methylcrotonyl-CoA carboxylase deficiency. in The Journal of biological chemistry 2009 (PubMed)

  3. Human Polyclonal MCCC2 Primary Antibody for EIA, WB - ABIN453184 : Uematsu, Sakamoto, Sugawara, Kumagai, Morimoto, Yamaguchi, Hasegawa, Kobayashi, Ihara, Yoshino, Watanabe, Inokuchi, Yokoyama, Kiwaki, Nakamura, Endo, Tsuchiya, Ohura: Novel mutations in five Japanese patients with 3-methylcrotonyl-CoA carboxylase deficiency. in Journal of human genetics 2007 (PubMed)

More Antibodies against Methylcrotonoyl-CoA Carboxylase 2 (Beta) Interaction Partners

Human Methylcrotonoyl-CoA Carboxylase 2 (Beta) (MCCC2) interaction partners

  1. Novel mutation in MCCC2 gene was identified in Chinese population.

  2. Mutation in 3-methylcrotonyl CoA carboxylase 2 gene is associated with 3-methylcrotonyl-CoA carboxylase deficiency.

  3. study reports eight different mutant alleles of MCCC1 (show MCCC1 Antibodies) or MCCC2 including six novel mutations in Korean patients with 3-methylcrotonyl-CoA carboxylase (MCC (show MCC Antibodies)) deficiency

  4. identified two novel MCCA (show MCCC1 Antibodies) and four novel MCCB (show MCCC1 Antibodies) mutant alleles from five MCC (show MCC Antibodies)-deficient patients

  5. factors other than the genotype at the MCCA (show MCCC1 Antibodies) and MCCB (show MCCC1 Antibodies) loci have a major influence on the phenotype of MCC (show MCC Antibodies) deficiency

  6. The Kd value of soraphen A for the BC domains of human ACC1 and ACC2 is 1 nM. This high binding affinity is mainly due to the extensive interactions between soraphen A and the human biotin carboxylase domain

  7. Molecular analyses revealed novel mutations in one of the causative genes, MCCA (show MCCC1 Antibodies) or MCCB (show MCCC1 Antibodies), in all five of the MCC (show MCC Antibodies) deficiency patients

Arabidopsis thaliana Methylcrotonoyl-CoA Carboxylase 2 (Beta) (MCCC2) interaction partners

  1. Studies indicate that mutations in either 3-methylcrotonyl CoA carboxylase MCCA (show MCCC1 Antibodies) (At1g03090) or MCCB (At4g34030) block mitochondrial Leu catabolism, as inferred from the increased accumulation of Leu.

Methylcrotonoyl-CoA Carboxylase 2 (Beta) (MCCC2) Antigen Profile

Protein Summary

This gene encodes the small subunit of 3-methylcrotonyl-CoA carboxylase. This enzyme functions as a heterodimer and catalyzes the carboxylation of 3-methylcrotonyl-CoA to form 3-methylglutaconyl-CoA. Mutations in this gene are associated with 3-Methylcrotonylglycinuria, an autosomal recessive disorder of leucine catabolism.

Gene names and symbols associated with MCCC2

  • methylcrotonoyl-Coenzyme A carboxylase 2 (beta) (mccc2) antibody
  • methylcrotonoyl-CoA carboxylase 2 (beta) (MCCC2) antibody
  • methylcrotonoyl-CoA carboxylase 2 (beta) (mccc2) antibody
  • methylcrotonoyl-CoA carboxylase 2 (beta) (Mccc2) antibody
  • methylcrotonoyl-CoA carboxylase beta chain (MCCB) antibody
  • methylcrotonoyl-Coenzyme A carboxylase 2 (beta) (Mccc2) antibody
  • 3-methylcrotonyl-CoA carboxylase antibody
  • 4930552N12Rik antibody
  • F28A23.210 antibody
  • F28A23_210 antibody
  • MCCB antibody
  • si:dkey-57m14.1 antibody
  • zgc:85685 antibody

Protein level used designations for MCCC2

methylcrotonoyl-CoA carboxylase beta chain, mitochondrial , methylcrotonoyl-Coenzyme A carboxylase 2 (beta) , methylcrotonoyl-CoA carboxylase 2 (beta) , methylcrotonoyl-CoA carboxylase beta chain, mitochondrial-like , 3-methylcrotonyl-CoA carboxylase 2 , 3-methylcrotonyl-CoA carboxylase non-biotin-containing subunit , 3-methylcrotonyl-CoA:carbon dioxide ligase subunit beta , MCCase subunit beta , biotin carboxylase , non-biotin containing subunit of 3-methylcrotonyl-CoA carboxylase

GENE ID SPECIES
405863 Danio rerio
427395 Gallus gallus
461823 Pan troglodytes
478091 Canis lupus familiaris
595048 Xenopus (Silurana) tropicalis
701211 Macaca mulatta
100037195 Xenopus laevis
100414949 Callithrix jacchus
64087 Homo sapiens
361884 Rattus norvegicus
829549 Arabidopsis thaliana
78038 Mus musculus
Selected quality suppliers for anti-Methylcrotonoyl-CoA Carboxylase 2 (Beta) (MCCC2) Antibodies
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