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anti-Optic Atrophy 3 (Autosomal Recessive, with Chorea and Spastic Paraplegia) (OPA3) Antibodies

The mouse ortholog of this protein co-purifies with the mitochondrial inner membrane. Additionally we are shipping OPA3 Proteins (5) and many more products for this protein.

list all antibodies Gene Name GeneID UniProt
OPA3 80207 Q9H6K4
OPA3    
OPA3    
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Top anti-OPA3 Antibodies at antibodies-online.com

Showing 10 out of 18 products:

Catalog No. Reactivity Host Conjugate Application Images Quantity Supplier Delivery Price Details
Human Rabbit Un-conjugated WB WB Suggested Anti-OPA3 Antibody Titration: 0.2-1 ug/mlELISA Titer: 1:62500Positive Control: Human kidney WB Suggested Anti-OPA3  Antibody Titration: 0.2-1 µg/mL ELISA Titer: 1:.2500  Positive Control: Human kidney 100 μL Log in to see 2 to 3 Days
$289.00
Details
Human Mouse Un-conjugated WB Western Blot analysis of OPA3 expression in transfected 293T cell line by OPA3 MaxPab polyclonal antibody.Lane 1: OPA3 transfected lysate(19.69 KDa).Lane 2: Non-transfected lysate. 50 μg Log in to see 9 Days
$430.00
Details
Human Rabbit Un-conjugated WB 50 μg Log in to see 8 to 10 Days
$551.83
Details
Human Mouse Un-conjugated ELISA, WB Western Blot detection against Immunogen (34.21 KDa) . 200 μL Log in to see 9 Days
$430.00
Details
Human Rabbit Un-conjugated IHC, WB   100 μL Log in to see 14 Days
$369.79
Details
Human Rabbit Un-conjugated IHC, WB   100 μL Log in to see 14 Days
$527.15
Details
Human Rabbit Un-conjugated IHC, ELISA, WB   50 μL Log in to see 9 to 11 Days
$313.50
Details
Human Rabbit Un-conjugated IHC, WB   200 μL Log in to see 9 Days
$487.50
Details
Human Mouse Un-conjugated ELISA, WB   50 μg Log in to see 11 to 16 Days
$553.14
Details
Human Mouse Un-conjugated WB   50 μg Log in to see 11 to 16 Days
$553.14
Details

OPA3 Antibodies by Reactivity, Application, Clonality and Conjugate

Attributes Applications Host Clonality
Human
,
,
Mouse (Murine)


Rat (Rattus)


Top referenced anti-OPA3 Antibodies

  1. Human Polyclonal OPA3 Primary Antibody for WB - ABIN529218 : Powell, Davies, Taylor, Wride, Votruba: Mitochondrial localization and ocular expression of mutant Opa3 in a mouse model of 3-methylglutaconicaciduria type III. in Investigative ophthalmology & visual science 2011 (PubMed)

More Antibodies against OPA3 Interaction Partners

Human Optic Atrophy 3 (Autosomal Recessive, with Chorea and Spastic Paraplegia) (OPA3) interaction partners

  1. Mutations of the OPA3 gene can cause either autosomal dominant or autosomal recessive optic atrophy.

  2. Report the results of a comprehensive study on OPA3 mutations, including the mutation spectrum and its prevalence in a large cohort of ADOA patients, the associated clinical phenotype and the functional characterisation of a newly identified OPA3 mutant.

  3. A novel missense mutation identifies OPA3 as the cause of a complex neurological disorder with marked lower limb dystonia.

  4. OPA1 mutations are the most common genetic defects identified in patients with suspected Autosomal-dominant optic atrophy (DOA), whereas OPA3 mutations are very rare in isolated optic atrophy cases.

  5. OPA3, as an integral mitochondrial outer membane perotein, has a crucial role in mitochondrial fission, and provides a direct link between mitochondrial morphology and optic atrophy.

  6. two missense mutations in OPA3 in two families affected by autosomal dominant optic atrophy and cataract (ADOAC)

  7. OPA1 mutations, mtDNA mutations, and OPA3 mutations in 980 patients Leber's hereditary optic neuropathy and autosomal dominant optic atrophy

  8. The mouse ortholog of OPA3 purifies with mitochondrial inner membranes.

  9. The mouse ortholog of OPA3 purifies with mitochondria

  10. type III 3-methylglutaconic aciduria (optic atrophy plus syndrome, or Costeff optic atrophy syndrome): identification of the OPA3 gene and its founder mutation in Iraqi Jews

Zebrafish Optic Atrophy 3 (Autosomal Recessive, with Chorea and Spastic Paraplegia) (OPA3) interaction partners

  1. mitochondrial OPA3 is required to limit HMG-CoA-derived MGC and protect the electron transport chain against inhibitory compounds in a zebrafish model of Costeff Syndrome

Cow (Bovine) Optic Atrophy 3 (Autosomal Recessive, with Chorea and Spastic Paraplegia) (OPA3) interaction partners

  1. The present study is the first report of the OPA3 mutation in dilated cardiomyopathy affected cows outside Switzerland.

  2. the nonsense mutation c.343C>T in the bovine OPA3 gene causes the late-onset dilated cardiomyopathy in Red Holstein cattle.

OPA3 Antigen Profile

Protein Summary

The mouse ortholog of this protein co-purifies with the mitochondrial inner membrane. Mutations in this gene have been shown to result in 3-methylglutaconic aciduria type III and autosomal dominant optic atrophy and cataract. Multiple transcript variants encoding different isoforms have been found for this gene.

Gene names and symbols associated with OPA3

  • optic atrophy 3 (autosomal recessive, with chorea and spastic paraplegia) (OPA3) antibody
  • optic atrophy 3 (opa3) antibody
  • MGA3 antibody

Protein level used designations for OPA3

Optic atrophy 3 (Iraqi-Jewish 'optic atrophy plus') , optic atrophy 3 protein , optic atrophy 3 protein homolog , mitochondrial optic atrophy 3 protein

GENE ID SPECIES
80207 Homo sapiens
497278 Danio rerio
523579 Bos taurus
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