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Succinate-CoA Ligase, alpha Subunit (SUCLG1) ELISA Kits

SUCLG1 encodes the alpha subunit of the heterodimeric enzyme succinate coenzyme A ligase. Additionally we are shipping Succinate-CoA Ligase, alpha Subunit Antibodies (21) and Succinate-CoA Ligase, alpha Subunit Proteins (7) and many more products for this protein.

list all ELISA KIts Gene Name GeneID UniProt
Anti-Human SUCLG1 SUCLG1 8802 P53597
Anti-Rat SUCLG1 SUCLG1 114597 P13086
Anti-Mouse SUCLG1 SUCLG1 56451 Q9WUM5
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More ELISA Kits for Succinate-CoA Ligase, alpha Subunit Interaction Partners

Human Succinate-CoA Ligase, alpha Subunit (SUCLG1) interaction partners

  1. First Chinese report of succinyl-CoA ligase (show SUCLG2 ELISA Kits) deficiency caused by novel SUCLG1 mutations; five novel pathogenic mutations in SUCLG1 were identified

  2. 3 novel mutations have been identified in patients with the mitochondrial DNA depletion syndrome (c.1048G>A and c.1049G>T in SUCLA2 (show SUCLA2 ELISA Kits) and c.531+4A>T in SUCLG1).

  3. Our results suggest that SUCLG1 mutations that lead to complete absence of SUCLG1 protein are responsible for a very severe disorder with antenatal manifestations, whereas a SUCLA2 (show SUCLA2 ELISA Kits)-like phenotype is found in patients with residual SUCLG1 protein.

  4. This report enlarges the phenotypic spectrum of SUCLG1 mutations and confirms that a characteristic metabolic profile (presence of MMA (show MMD ELISA Kits) and C4-DC carnitine in urines) and basal ganglia MRI (show C7ORF49 ELISA Kits) lesions are the hallmarks of SCS (show TWIST1 ELISA Kits) defects.

  5. A novel mutation in the SUCLG1 gene was found in two newborns having lethal lactic acidosis, multi-organ failure and congenital malformations including interrupted aortic arch.

Pig (Porcine) Succinate-CoA Ligase, alpha Subunit (SUCLG1) interaction partners

  1. Structure of GTP-specific succinyl-CoA synthetase subunits in complex with CoA has been resolved.

  2. succinyl-CoA (show OXCT1 ELISA Kits) synthetase is able to protect GTP (show AK3 ELISA Kits) from hydrolysis when the active-site histidine residue is not in position to be phosphorylated

Mouse (Murine) Succinate-CoA Ligase, alpha Subunit (SUCLG1) interaction partners

  1. ADP and GDP succinyl-CoA (show OXCT1 ELISA Kits) synthetases have different expression patterns and specificity

Succinate-CoA Ligase, alpha Subunit (SUCLG1) Antigen Profile

Antigen Summary

This gene encodes the alpha subunit of the heterodimeric enzyme succinate coenzyme A ligase. This enzyme is targeted to the mitochondria and catalyzes the conversion of succinyl CoA and ADP or GDP to succinate and ATP or GTP. Mutations in this gene are the cause of the metabolic disorder fatal infantile lactic acidosis and mitochondrial DNA depletion.

Gene names and symbols associated with SUCLG1

  • succinate-CoA ligase, alpha subunit (SUCLG1) antibody
  • succinate-CoA ligase, alpha subunit (suclg1) antibody
  • succinate-CoA ligase, alpha subunit (Suclg1) antibody
  • succinate-CoA ligase, GDP-forming, alpha subunit (suclg1) antibody
  • succinate-CoA ligase, GDP-forming, alpha subunit (Suclg1) antibody
  • 1500000I01Rik antibody
  • GALPHA antibody
  • MTDPS9 antibody
  • SCS antibody
  • Sucla1 antibody
  • zgc:92738 antibody
  • zgc:103729 antibody

Protein level used designations for SUCLG1

succinate-CoA ligase, GDP-forming, alpha subunit , succinate-CoA ligase, GDP-forming alpha subunit , SCS-alpha , succinyl-CoA ligase [ADP/GDP-forming] subunit alpha, mitochondrial , succinyl-CoA ligase [GDP-forming] subunit alpha, mitochondrial , succinyl-CoA synthetase subunit alpha , succinyl-CoA synthetase alpha subunit , SUCLGa

GENE ID SPECIES
470417 Pan troglodytes
475775 Canis lupus familiaris
494796 Xenopus laevis
594977 Xenopus (Silurana) tropicalis
8802 Homo sapiens
399539 Sus scrofa
114597 Rattus norvegicus
509983 Bos taurus
436850 Danio rerio
56451 Mus musculus
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