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Ureidopropionase, beta Proteins (UPB1)

UPB1 encodes a protein that belongs to the CN hydrolase family. Additionally we are shipping UPB1 Antibodies (13) and UPB1 Kits (1) and many more products for this protein.

list all proteins Gene Name GeneID UniProt
UPB1 51733 Q9UBR1
UPB1 103149 Q8VC97
Rat UPB1 UPB1 116593 Q03248
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Top UPB1 Proteins at

Showing 5 out of 8 products:

Catalog No. Origin Source Conjugate Images Quantity Supplier Delivery Price Details
HOST_Escherichia coli (E. coli) Human His tag „Crystallography Grade“ protein due to multi-step, protein-specific pu... 1 mg Log in to see 29 to 34 Days
HOST_Escherichia coli (E. coli) Mouse His tag „Crystallography Grade“ protein due to multi-step, protein-specific pu... 1 mg Log in to see 29 to 34 Days
HOST_Wheat germ Human GST tag 10 μg Log in to see 9 Days
HOST_Escherichia coli (E. coli) Human His tag   50 μg Log in to see 5 Days
HOST_Human Human Un-conjugated   20 μg Log in to see 9 to 11 Days

UPB1 Proteins by Origin and Source

Origin Expressed in Conjugate
Human , ,
Mouse (Murine)

More Proteins for Ureidopropionase, beta (UPB1) Interaction Partners

Human Ureidopropionase, beta (UPB1) interaction partners

  1. The c.977G>A (p.R326Q) is the most common mutation of the UPB1 gene in Chinese. The predicted incidence indicates that beta-ureidopropionase deficiency is significantly underdiagnosed in the Chinese population.

  2. This study reports the clinical, biochemical, and molecular analysis of a newly identified patient with beta-ureidopropionase deficiency and the effect of the first synonymous mutation in UBP1 (show UBP1 Proteins) affecting pre-mRNA splicing, using the minigene approach.

  3. analysis of UPB1 variants on 5-FU-related toxicity in the population of all analyzed patients revealed an association between the c.-80C>G (rs2070474) variant and gastrointestinal toxicity

  4. An altered homeostasis of beta-aminoisobutyric acid and/or increased oxidative stress might contribute to some of the clinical abnormalities encountered in patients with a beta (show SUCLA2 Proteins)-ureidopropionase deficiency.

  5. analysis of the beta-ureidopropionase gene (UPB1) of the first 4 patients presenting with a complete enzyme deficiency, revealed the presence of 2 splice-site mutations (IVS1-2A>G and IVS8-1G>A) and one missense mutation (A85E)

Mouse (Murine) Ureidopropionase, beta (UPB1) interaction partners

UPB1 Protein Profile

Protein Summary

This gene encodes a protein that belongs to the CN hydrolase family. Beta-ureidopropionase catalyzes the last step in the pyrimidine degradation pathway. The pyrimidine bases uracil and thymine are degraded via the consecutive action of dihydropyrimidine dehydrogenase (DHPDH), dihydropyrimidinase (DHP) and beta-ureidopropionase (UP) to beta-alanine and beta-aminoisobutyric acid, respectively. UP deficiencies are associated with N-carbamyl-beta-amino aciduria and may lead to abnormalities in neurological activity.

Gene names and symbols associated with Ureidopropionase, beta Proteins (UPB1)

  • ureidopropionase, beta (upb1)
  • ureidopropionase, beta (UPB1)
  • Protein UPB-1 (upb-1)
  • ureidopropionase, beta (Upb1)
  • AI195023 protein
  • Bup1 protein
  • MGC82230 protein
  • wu:fb69e03 protein
  • zgc:64020 protein

Protein level used designations for Ureidopropionase, beta Proteins (UPB1)

ureidopropionase, beta , beta-ureidopropionase , beta-alanine synthase , N-carbamoyl-beta-alanine amidohydrolase , beta-ureidopropionase-like , BUP-1 , n-carbamoyl-beta-alanine amidohydrolase

447326 Xenopus laevis
504557 Bos taurus
707752 Macaca mulatta
747532 Pan troglodytes
100013001 Monodelphis domestica
100053177 Equus caballus
100145317 Xenopus (Silurana) tropicalis
100155919 Sus scrofa
100172385 Pongo abelii
100357276 Oryctolagus cuniculus
100478175 Ailuropoda melanoleuca
100597745 Nomascus leucogenys
174040 Caenorhabditis elegans
322660 Danio rerio
416949 Gallus gallus
51733 Homo sapiens
486398 Canis lupus familiaris
103149 Mus musculus
116593 Rattus norvegicus
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