FKRP antibody (C-Term)

Catalog No. ABIN1536611

Product Details anti-FKRP Antibody

Target: FKRP (Fukutin Related Protein (FKRP))

Binding Specificity: AA 418-444, C-Term

Reactivity: Human

Host: Mouse

Clonality: Monoclonal

Conjugate: This FKRP antibody is un-conjugated

Application: Western Blotting (WB)

Predicted Reactivity: M

Purification: This antibody is purified through a protein G column, followed by dialysis against PBS.

Immunogen: This FKRP antibody is generated from mice immunized with a KLH conjugated synthetic peptide between 418-444 amino acids from the C-terminal region of human FKRP.

Clone: 386CT13-1-9

Isotype: IgG1

Application Details

Application Notes: WB: 1:100

Restrictions: For Research Use only

Handling

Format: Liquid

Buffer: Purified monoclonal antibody supplied in PBS with 0.09 % (W/V) sodium azide.

Preservative: Sodium azide

Precaution of Use: This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Storage: 4 °C,-20 °C

Storage Comment: FKRP Antibody (C-term) can be refrigerated at 2-8 °C for up to 6 months. For long term storage, keep at -20 °C.

Expiry Date: 6 months

Target Details for FKRP

Target: FKRP (Fukutin Related Protein (FKRP))

Alternative Name: FKRP (FKRP Products)

Synonyms: zgc:162829 antibody, LGMD2I antibody, MDC1C antibody, MDDGA5 antibody, MDDGB5 antibody, MDDGC5 antibody, A830029B19Rik antibody, AI842067 antibody, AI847300 antibody, LGMD1I antibody, fukutin related protein antibody, FKRP antibody, fkrp antibody, Fkrp antibody

Background: This gene encodes a protein which is targeted to the medial Golgi apparatus and is necessary for posttranslational modification of dystroglycan. Mutations in this gene have been associated with congenital muscular dystrophy, mental retardation, and cerebellar cysts. Several alternatively spliced transcript variants of this gene have been described, but the full-length nature of some of these variants has not been determined. [provided by RefSeq].

Molecular Weight: 54568

Gene ID: 79147

NCBI Accession: NP_001034974, NP_077277

UniProt: Q9H9S5

Pathways: Regulation of Carbohydrate Metabolic Process