MMAA antibody (N-Term)

Catalog No. ABIN653752

Product Details anti-MMAA Antibody

Target: MMAA (Methylmalonic Aciduria (Cobalamin Deficiency) Type A (MMAA))

Binding Specificity: AA 56-84, N-Term

Reactivity: Human, Mouse

Host: Rabbit

Clonality: Polyclonal

Conjugate: This MMAA antibody is un-conjugated

Application: Western Blotting (WB), Immunohistochemistry (Paraffin-embedded Sections) (IHC (p))

Purification: This antibody is purified through a protein A column, followed by peptide affinity purification.

Immunogen: This MMAA antibody is generated from rabbits immunized with a KLH conjugated synthetic peptide between 56-84 amino acids from the N-terminal region of human MMAA.

Clone: RB24782

Isotype: Ig Fraction

Application Details

Application Notes: WB: 1:500. WB: 1:1000. IHC-P: 1:50~100

Restrictions: For Research Use only

Handling

Format: Liquid

Buffer: Purified polyclonal antibody supplied in PBS with 0.09 % (W/V) sodium azide.

Preservative: Sodium azide

Precaution of Use: This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Storage: 4 °C,-20 °C

Storage Comment: Maintain refrigerated at 2-8 °C for up to 6 months. For long term storage store at -20 °C in small aliquots to prevent freeze-thaw cycles.

Expiry Date: 6 months

Target Details for MMAA

Target: MMAA (Methylmalonic Aciduria (Cobalamin Deficiency) Type A (MMAA))

Alternative Name: MMAA (MMAA Products)

Synonyms: 2810018E08Rik antibody, AI840684 antibody, cblA antibody, methylmalonic aciduria (cobalamin deficiency) type A antibody, methylmalonic aciduria (cobalamin deficiency) cblA type antibody, Mmaa antibody, MMAA antibody

Background: The protein encoded by this gene is involved in the translocation of cobalamin into the mitochondrion, where it is used in the final steps of adenosylcobalamin synthesis. Adenosylcobalamin is a coenzyme required for the activity of methylmalonyl-CoA mutase. Defects in this gene are a cause of methylmalonic aciduria.

Molecular Weight: 46538

Gene ID: 166785

NCBI Accession: NP_758454

UniProt: Q8IVH4

Pathways: Monocarboxylic Acid Catabolic Process