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BCKDHB antibody (N-Term)

BCKDHB Reactivity: Human WB, FACS, IF, IHC (p), EIA Host: Rabbit Polyclonal unconjugated
Catalog No. ABIN950620
  • Target See all BCKDHB Antibodies
    BCKDHB (Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB))
    Binding Specificity
    • 8
    • 8
    • 6
    • 1
    • 1
    AA 44-74, N-Term
    Reactivity
    • 18
    • 2
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    Human
    Host
    • 18
    Rabbit
    Clonality
    • 18
    Polyclonal
    Conjugate
    • 8
    • 2
    • 2
    • 2
    • 2
    • 2
    This BCKDHB antibody is un-conjugated
    Application
    • 18
    • 14
    • 13
    • 13
    • 13
    • 5
    • 2
    Western Blotting (WB), Flow Cytometry (FACS), Immunofluorescence (IF), Immunohistochemistry (Paraffin-embedded Sections) (IHC (p)), Enzyme Immunoassay (EIA)
    Specificity
    This antibody reacts to BCKDHB.
    Cross-Reactivity (Details)
    Species reactivity (tested):Human.
    Purification
    Affinity chromatography on Protein A
    Immunogen
    KLH conjugated synthetic peptide between 44-74 amino acids from the N-terminal region of human BCKDHB
    Isotype
    Ig Fraction
    Top Product
    Discover our top product BCKDHB Primary Antibody
  • Application Notes
    Optimal working dilution should be determined by the investigator.
    Restrictions
    For Research Use only
  • Format
    Liquid
    Concentration
    0.25 mg/mL
    Buffer
    PBS containing 0.09 % (W/V) sodium azide as preservative
    Preservative
    Sodium azide
    Precaution of Use
    This product contains sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
    Handling Advice
    Avoid repeated freezing and thawing.
    Storage
    4 °C/-20 °C
    Storage Comment
    Store the antibody undiluted at 2-8 °C for one month or (in aliquots) at -20 °C for longer.
  • Target
    BCKDHB (Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB))
    Alternative Name
    BCKDHB (BCKDHB Products)
    Synonyms
    zgc:158777 antibody, BCKDHB antibody, E1B antibody, dJ279A18.1 antibody, branched chain keto acid dehydrogenase E1, beta polypeptide antibody, branched chain keto acid dehydrogenase E1 subunit beta antibody, branched chain keto acid dehydrogenase E1, beta polypeptide S homeolog antibody, branched chain ketoacid dehydrogenase E1, beta polypeptide antibody, BCKDHB antibody, bckdhb antibody, bckdhb.S antibody, Bckdhb antibody
    Background
    Branched-chain keto acid dehydrogenase is a multienzyme complex associated with the inner membrane of mitochondria, and functions in the catabolism of branched-chain amino acids. The complex consists of multiple copies of 3 components: branched-chain alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2) and lipoamide dehydrogenase (E3). This gene encodes the E1 beta subunit, and mutations therein have been associated with maple syrup urine disease (MSUD), type 1B, a disease characterized by a maple syrup odor to the urine in addition to mental and physical retardation, and feeding problems.Synonyms: 2-oxoisovalerate dehydrogenase subunit beta, alpha-keto acid dehydrogenase, mitochondrial Branched-chain alpha-keto acid dehydrogenase E1 component beta chain
    Gene ID
    594
    NCBI Accession
    NP_000047
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