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Acyl-CoA Dehydrogenase, Very Long Chain ELISA Kits (ACADVL)
On are 0 Acyl-CoA Dehydrogenase, Very Long Chain (ACADVL) ELISA Kits from different suppliers available. Additionally we are shipping ACADVL Antibodies (77) and ACADVL Proteins (12) and many more products for this protein. A total of 98 ACADVL products are currently listed.
ACAD6, fb52d04, LCACD, vlcad, wu:fb52d04, wu:fc75e01, zgc:64067
list all ELISA KIts Gene Name GeneID UniProt
Human ACADVL ACADVL 37 P49748
Rat ACADVL ACADVL 25363 P45953
Mouse ACADVL ACADVL 11370 P50544

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More ELISA Kits for ACADVL Interaction Partners

Human Acyl-CoA Dehydrogenase, Very Long Chain (ACADVL) interaction partners

  1. LCHAD (show HADHA ELISA Kits) and MCAD are differentially expressed in maternal and fetal tissues during normal late pregnancy, which may represent a metabolic adaptation in response to physiological maternal dyslipidemia during late pregnancy.

  2. 11 mutations in ACADVL gene in 7 patients, 7 reported (p.S22X, p.W427X, p.A213T, p.G222R, p.R450H, c.296-297delCA, c.1605+1G>T), 4 novel (p.S72F, p.Q100X, p.M437T, p.D466Y). p.R450H and p.D466Y (14.28%, 2/14 alleles) mutations identified in 2 alleles.

  3. Case Report: missense mutation within the ACADVL gene responsible for very-long-chain acyl-CoA dehydrogenase deficiency and sudden infant death.

  4. These results emphasize the importance of functional investigation of abnormal NBS (show NBN ELISA Kits) or clinical testing suggestive but not diagnostic of very-long-chain acyl-CoA dehydrogenase .

  5. These findings support the importance of considering that mutations may be present in the ACADVL gene when a significant partial deficiency is found in CPTII (show CPT2 ELISA Kits) activity, but no mutations in the CPT2 (show CPT2 ELISA Kits) gene can be identified.

  6. Identification of 2 VLCAD mutations leads to precautions in the management of the children with VLCAD deficiency.

  7. The expressions of LCHAD (show HADHA ELISA Kits) gene and protein are remarkably reduced in early onset severe preeclampsia and HELLP syndrome.

  8. Analyzed potential rhabdomyolysis-susceptibility genes (RYR 1 (show RYR1 ELISA Kits), CPT II (show CPT2 ELISA Kits), VLCAD and CYP (show PPIG ELISA Kits) 2D6) from autopsy samples of methamphetamine abusers; no obvious relationship between the genetic mutations observed in this study and rhabdomyolysis was seen.

  9. Down regulation of ACADVL is associated with cervical squamous cell carcinoma.

  10. Missense mutations in Very-Long-Chain Acyl-CoA Dehydrogenase is associated with inborn errors of lipid metabolism.

Cow (Bovine) Acyl-CoA Dehydrogenase, Very Long Chain (ACADVL) interaction partners

  1. Bovine ACADVL gene had a significant effect on chest width (P<0.05), chest depth (P<0.05), and hip width (P<0.05) in the Qinchuan breed.

Mouse (Murine) Acyl-CoA Dehydrogenase, Very Long Chain (ACADVL) interaction partners

  1. Triheptanoin was not able to prevent the development of systolic dysfunction in VLCAD(-/-) mice despite an upregulation of cardiac glucose oxidation. Strikingly, the anaplerotic effects of triheptanoin were restricted to the liver.

  2. observed strong upregulation of peroxisomal beta-oxidation in VLCAD(-/-) mice

  3. SIRT3 (show SIRT3 ELISA Kits) and SIRT5 (show SIRT5 ELISA Kits) regulate the enzyme activity and cardiolipin binding of very long-chain acyl-CoA dehydrogenase

  4. Studies conducted with permeabilized mitochondria and different chain length acyl-CoA (show GNPAT ELISA Kits) derivatives suggest that VLCAD is also a source of reactive oxygen species production in mitochondria of high fat diet animals.

  5. We demonstrate here that both dietary interventions with respect to the fat content of the diet reverse endogenous compensatory mechanisms in muscle that have evolved in VLCAD(-/-) mice resulting in pronounced energy deficiency

  6. VLCAD(-/-) mice develop tissue-specific strategies to compensate deficiency of VLCAD either by induction of other mitochondrial acyl-CoA (show GNPAT ELISA Kits) dehydrogenases or by enhancement of glucose oxidation.

  7. Report a longer QTc interval and lipid alterations in VLCAD null mice.

  8. Four VLCAD-/- deficient mice died unexpectedly on the treadmill during the early stages of training. The VLCAD-/- deficient mice that survived adapted to the aerobic interval training similarly to the non-deficient mice.

  9. Medium-chain triglycerides impair lipid metabolism and induce hepatic steatosis in very long-chain acyl-CoA dehydrogenase (VLCAD)-deficient mice

  10. Data show that in VLCAD knockout mice fed a long-chain triglyceride diet, fasting results in accumulation of liver lipids, hepatopathy and upregulation of peroxisomal and microsomal oxidation pathways as well as antioxidant enzyme activities and TBARS.

ACADVL Antigen Profile

Antigen Summary

The protein encoded by this gene is targeted to the inner mitochondrial membrane where it catalyzes the first step of the mitochondrial fatty acid beta-oxidation pathway. This acyl-Coenzyme A dehydrogenase is specific to long-chain and very-long-chain fatty acids. A deficiency in this gene product reduces myocardial fatty acid beta-oxidation and is associated with cardiomyopathy. Alternative splicing results in multiple transcript variants encoding different isoforms.

Alternative names and synonyms associated with ACADVL

  • acyl-CoA dehydrogenase, very long chain (ACADVL) Elisa Kit
  • acyl-CoA dehydrogenase, very long chain (Acadvl) Elisa Kit
  • acyl-Coenzyme A dehydrogenase, very long chain (acadvl) Elisa Kit
  • acyl-Coenzyme A dehydrogenase, very long chain (Acadvl) Elisa Kit
  • ACAD6 Elisa Kit
  • fb52d04 Elisa Kit
  • LCACD Elisa Kit
  • vlcad Elisa Kit
  • wu:fb52d04 Elisa Kit
  • wu:fc75e01 Elisa Kit
  • zgc:64067 Elisa Kit

Protein level used designations for ACADVL

acyl-Coenzyme A dehydrogenase, very long chain , very long-chain specific acyl-CoA dehydrogenase, mitochondrial , VLCAD , acyl-coenzyme A dehydrogenase, very long chain , VLCAD very-long-chain acyl-CoA dehydrogenase , Very long chain Acyl-Coa dehydrogenase , vlcad , MVLCAD

100061583 Equus caballus
37 Homo sapiens
489463 Canis lupus familiaris
282130 Bos taurus
25363 Rattus norvegicus
573723 Danio rerio
11370 Mus musculus
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