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ETHE1 Protein (AA 13-254) (His tag)

ETHE1 Origin: Human Host: Escherichia coli (E. coli) Recombinant > 90 % by SDS - PAGE SDS
Catalog No. ABIN668013
  • Target See all ETHE1 Proteins
    ETHE1 (Ethylmalonic Encephalopathy 1 (ETHE1))
    Protein Type
    Recombinant
    Protein Characteristics
    AA 13-254
    Origin
    • 6
    • 1
    • 1
    Human
    Source
    • 2
    • 2
    • 2
    • 1
    • 1
    Escherichia coli (E. coli)
    Purification tag / Conjugate
    This ETHE1 protein is labelled with His tag.
    Application
    SDS-PAGE (SDS)
    Characteristics
    ETHE1, 13-254aa, Human, His tag, E.coli
    Purity
    > 90 % by SDS - PAGE
    Top Product
    Discover our top product ETHE1 Protein
  • Restrictions
    For Research Use only
  • Format
    Liquid
    Concentration
    1.0 mg/ml (determined by Bradford assay)
    Buffer
    Liquid. 20mM Tris-HCl buffer (pH8.0) containing 10% glycerol, 0.1M NaCl
    Storage
    4 °C
  • Target
    ETHE1 (Ethylmalonic Encephalopathy 1 (ETHE1))
    Alternative Name
    ETHE1 (ETHE1 Products)
    Synonyms
    zgc:85680 Protein, HSCO Protein, YF13H12 Protein, 0610025L15Rik Protein, Hsco Protein, ETHE1, persulfide dioxygenase Protein, ethylmalonic encephalopathy 1 Protein, Ethe1 Protein, ethe1 Protein, ETHE1 Protein
    Background
    ETHE1 is a mitochondrial sulfur dioxygenase involved in catabolism of sulfide that accumulates to toxic levels in ethylmalonic encephalopathy. Mutations of ETHE1 were detected in all the typical ethylmalonic encephalopathy patients analysed, but no ETHE1 mutations were identified in patients presenting with early onset progressive encephalopathy with ethylmalonic aciduria. Recombinant human ETHE1 protein, fused to His-tag at N-terminus, was expressed in E.coli and purified by using conventional chromatography. Synonyms: Protein ETHE1, mitochondrial,. NCBI no.: NP_055112
    Molecular Weight
    29.1 kDa(267aa) confirmed by MALDI-TOF
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