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BCKDHB antibody (N-Term)

BCKDHB Reactivity: Human WB, FACS, IF, IHC (p) Host: Rabbit Polyclonal RB20925 unconjugated
Catalog No. ABIN654629
  • Target See all BCKDHB Antibodies
    BCKDHB (Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB))
    Binding Specificity
    • 8
    • 7
    • 7
    • 1
    • 1
    AA 41-70, N-Term
    Reactivity
    • 18
    • 2
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    Human
    Host
    • 18
    Rabbit
    Clonality
    • 18
    Polyclonal
    Conjugate
    • 8
    • 2
    • 2
    • 2
    • 2
    • 2
    This BCKDHB antibody is un-conjugated
    Application
    • 18
    • 14
    • 13
    • 13
    • 13
    • 5
    • 2
    • 1
    Western Blotting (WB), Flow Cytometry (FACS), Immunofluorescence (IF), Immunohistochemistry (Paraffin-embedded Sections) (IHC (p))
    Purification
    This antibody is purified through a protein A column, followed by peptide affinity purification.
    Immunogen
    This BCKDHB antibody is generated from rabbits immunized with a KLH conjugated synthetic peptide between 41-70 amino acids from the N-terminal region of human BCKDHB.
    Clone
    RB20925
    Isotype
    Ig Fraction
  • Application Notes
    IF: 1:25. WB: 1:1000. WB: 1:1000. IHC-P-Leica: 1:500. IHC-P-Leica: 1:500. FC: 1:10~50
    Restrictions
    For Research Use only
  • Format
    Liquid
    Buffer
    Purified polyclonal antibody supplied in PBS with 0.09 % (W/V) sodium azide.
    Preservative
    Sodium azide
    Precaution of Use
    This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
    Storage
    4 °C,-20 °C
    Storage Comment
    Maintain refrigerated at 2-8 °C for up to 6 months. For long term storage store at -20 °C in small aliquots to prevent freeze-thaw cycles.
    Expiry Date
    6 months
  • Target
    BCKDHB (Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB))
    Alternative Name
    BCKDHB (BCKDHB Products)
    Synonyms
    zgc:158777 antibody, BCKDHB antibody, E1B antibody, dJ279A18.1 antibody, branched chain keto acid dehydrogenase E1, beta polypeptide antibody, branched chain keto acid dehydrogenase E1 subunit beta antibody, branched chain keto acid dehydrogenase E1, beta polypeptide S homeolog antibody, branched chain ketoacid dehydrogenase E1, beta polypeptide antibody, BCKDHB antibody, bckdhb antibody, bckdhb.S antibody, Bckdhb antibody
    Background
    Branched-chain keto acid dehydrogenase is a multienzyme complex associated with the inner membrane of mitochondria, and functions in the catabolism of branched-chain amino acids. The complex consists of multiple copies of 3 components: branched-chain alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2) and lipoamide dehydrogenase (E3). This gene encodes the E1 beta subunit, and mutations therein have been associated with maple syrup urine disease (MSUD), type 1B, a disease characterized by a maple syrup odor to the urine in addition to mental and physical retardation, and feeding problems.
    Molecular Weight
    43122
    Gene ID
    594
    NCBI Accession
    NP_000047, NP_898871
    UniProt
    P21953
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