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BCKDHA antibody (AA 276-445)
BCKDHA
Reactivity: Human
WB
Host: Rabbit
Polyclonal
unconjugated
Product Details anti-BCKDHA Antibody
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Target
See all BCKDHA Antibodies
BCKDHA
(Branched Chain Keto Acid Dehydrogenase E1, alpha Polypeptide (BCKDHA))
Binding Specificity
All epitopes for BCKDHA antibodies
AA 276-445
Reactivity
All reactivities for BCKDHA antibodies
Human
Host
All hosts for BCKDHA antibodies
Rabbit
Clonality
All clonalities for BCKDHA antibodies
Polyclonal
Conjugate
All conjugates for BCKDHA antibodies
This BCKDHA antibody is un-conjugated
Application
All applications for BCKDHA antibodies
Western Blotting (WB)
Purpose
BCKDHA Rabbit pAb
Sequence
SEQYRGDGIA ARGPGYGIMS IRVDGNDVFA VYNATKEARR RAVAENQPFL IEAMTYRIGH HSTSDDSSAY RSVDEVNYWD KQDHPISRLR HYLLSQGWWD EEQEKAWRKQ SRRKVMEAFE QAERKPKPNP NLLFSDVYQE MPAQLRKQQE SLARHLQTYG EHYPLDHFDK
Cross-Reactivity
Human, Mouse, Rat
Characteristics
Polyclonal Antibodies
Purification
Affinity purification
Immunogen
Recombinant fusion protein containing a sequence corresponding to amino acids 276-445 of human BCKDHA (NP_000700.1).
Isotype
IgG
Top Product
Discover our top product BCKDHA Primary Antibody
Alternatives
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anti-Branched Chain Keto Acid Dehydrogenase E1, alpha Polypeptide (BCKDHA) (AA 71-120) antibody
BCKDHA
Reactivity: Human, Mouse, Rat, Rabbit, Guinea Pig, Sheep, Cow, Horse, Monkey, Pig, Xenopus laevis
WB
Host: Rabbit
Polyclonal
unconjugated
Application Details
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Application Notes
WB,1:500 - 1:2000
Restrictions
For Research Use only
Handling
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Format
Liquid
Buffer
PBS with 0.02 % sodium azide,50 % glycerol, pH 7.3.
Preservative
Sodium azide
Precaution of Use
This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
Storage
-20 °C
Storage Comment
Store at -20°C. Avoid freeze / thaw cycles.
Target Details for BCKDHA
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Target
BCKDHA
(Branched Chain Keto Acid Dehydrogenase E1, alpha Polypeptide (BCKDHA))
Alternative Name
BCKDHA (BCKDHA Products )
Synonyms
wu:fd20d04 antibody, zgc:110049 antibody, BCKDE1A antibody, MSU antibody, MSUD1 antibody, OVD1A antibody, BCKDA antibody, E1a antibody, 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial antibody, branched chain keto acid dehydrogenase E1, alpha polypeptide antibody, 2-oxoisovalerate dehydrogenase alpha subunit (branched-chain alpha-keto acid dehydrogenase E1 component alpha chain) (BCKDH E1-alpha) (BCKDE1A) antibody, branched chain ketoacid dehydrogenase E1, alpha polypeptide antibody, LOC704978 antibody, bckdha antibody, BCKDHA antibody, BckdhA antibody, Bckdha antibody
Background
The branched-chain alpha-keto acid (BCAA) dehydrogenase (BCKD) complex is an innter mitochondrial enzyme complex that catalyzes the second major step in the catabolism of the branched-chain amino acids leucine, isoleucine, and valine. The BCKD complex consists of three catalytic components: a heterotetrameric (alpha2-beta2) branched-chain alpha-keto acid decarboxylase (E1), a dihydrolipoyl transacylase (E2), and a dihydrolipoamide dehydrogenase (E3). This gene encodes the alpha subunit of the decarboxylase (E1) component. Mutations in this gene result in maple syrup urine disease, type IA. Multiple transcript variants encoding different isoforms have been found for this gene.,BCKDHA,BCKDE1A,MSU,MSUD1,OVD1A,BCKDHA
Molecular Weight
50kDa
Gene ID
593
UniProt
P12694
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