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Galactosylceramidase Products

(Galactosylceramidase (GALC))

Categories

This gene encodes a lysosomal protein which hydrolyzes the galactose ester bonds of galactosylceramide, galactosylsphingosine, lactosylceramide, and monogalactosyldiglyceride. Mutations in this gene have been associated with Krabbe disease, also known as globoid cell leukodystrophy. Alternate transcriptional splice variants, encoding different isoforms, have been characterized. [provided by RefSeq, Jul 2008].

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Featured Galactosylceramidase Categories

Galactosylceramidase Antibodies

High quality antibodies with extensive validation data.

Galactosylceramidase ELISA Kits

Reliable ELISA kits for a wide range of species.

Galactosylceramidase Proteins

Proteins for various applications incl. WB, ELISA, IF etc.

Recommended Galactosylceramidase Antibodies

Product
Reactivity
Application
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Application WB, IHC
Validations
  • (5)
Cat. No. ABIN1679950
Quantity 100 μg
Datasheet Datasheet
Reactivity Human
Application WB, IHC, IP, ICC
Validations
  • (4)
Cat. No. ABIN7438280
Quantity 100 μL
Datasheet Datasheet
Reactivity Rat
Application WB, ELISA
Validations
  • (4)
Cat. No. ABIN708101
Quantity 100 μL
Datasheet Datasheet

Recommended Galactosylceramidase ELISA Kits

Product
Reactivity
Analytical Method
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Analytical Method Quantitative Sandwich ELISA
Validations
  • (1)
Cat. No. ABIN6966934
Quantity 96 tests
Datasheet Datasheet
Reactivity Mouse
Analytical Method Quantitative Sandwich ELISA
Validations
Cat. No. ABIN5593339
Quantity 96 tests
Datasheet Datasheet
Reactivity Dog
Analytical Method
Validations
Cat. No. ABIN1134068
Quantity 96 tests
Datasheet Datasheet

Recommended Galactosylceramidase Proteins

Product
Reactivity
Source
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Source Wheat germ
Validations
  • (1)
Cat. No. ABIN1354704
Quantity 10 μg
Datasheet Datasheet
Reactivity Human
Source Wheat germ
Validations
  • (1)
Cat. No. ABIN1354706
Quantity 10 μg
Datasheet Datasheet
Reactivity Human
Source Wheat germ
Validations
  • (1)
Cat. No. ABIN1354708
Quantity 10 μg
Datasheet Datasheet

Latest Publications for our Galactosylceramidase products

Lee, Kang, Causevic, Herdt, Eckman, Eckman: "Molecular characterization of mutations that cause globoid cell leukodystrophy and pharmacological rescue using small molecule chemical chaperones." in: The Journal of neuroscience : the official journal of the Society for Neuroscience, Vol. 30, Issue 16, pp. 5489-97, (2010) (PubMed).

Adler, Fuchs, Kim, Kraft, King, Pelling, Ronai: "jun-NH2-terminal kinase activation mediated by UV-induced DNA lesions in melanoma and fibroblast cells." in: Cell growth & differentiation : the molecular biology journal of the American Association for Cancer Research, Vol. 6, Issue 11, pp. 1437-46, (1996) (PubMed).

Devary, Rosette, DiDonato, Karin: "NF-kappa B activation by ultraviolet light not dependent on a nuclear signal." in: Science (New York, N.Y.), Vol. 261, Issue 5127, pp. 1442-5, (1993) (PubMed).

Hibi, Lin, Smeal, Minden, Karin: "Identification of an oncoprotein- and UV-responsive protein kinase that binds and potentiates the c-Jun activation domain." in: Genes & development, Vol. 7, Issue 11, pp. 2135-48, (1993) (PubMed).

Synonyms and alternative names related to Galactosylceramidase

galactosylceramidase (GALC), galactosylceramidase (Galc), galactosylceramidase a (galca), galactosylceramidase (galc), Galactosylceramidase (Caci_7107), Galactosylceramidase (Bacsa_1415), Galactosylceramidase (Spico_0384), Galactosylceramidase (LOC100304802), galactosylceramidase L homeolog (galc.L), galactosylceramidase b (galcb), 2310068B06Rik, A930008M05Rik, AW212969, AW413532, Gacy, galc, GALCERase, galcl, si:ch211-199l3.4, twi, twitcher, wu:fi04e07, zgc:56444, zgc:92561

Protein level used designations for Galactosylceramidase

  • GALCERase
  • galactocerebrosidase
  • galactocerebroside beta-galactosidase
  • galactosylceramide beta-galactosidase
  • galactosylceraminidase
  • galactosylceramidase (Krabbe disease)
  • galactosylceramidase like
  • Galactosylceramidase
  • Galactocerebrosidase
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