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Browse our Isovaleryl-CoA Dehydrogenase Proteins (IVD)

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Isovaleryl-CoA Dehydrogenase Proteins (IVD)
On are 14 Isovaleryl-CoA Dehydrogenase (IVD) Proteins from 7 different suppliers available. Additionally we are shipping Isovaleryl-CoA Dehydrogenase Antibodies (33) and Isovaleryl-CoA Dehydrogenase Kits (4) and many more products for this protein. A total of 58 Isovaleryl-CoA Dehydrogenase products are currently listed.
1300016K07Rik, 6720455E18Rik, ACAD2, AI463340, ATIVD, isovaleryl-CoA-dehydrogenase, ISOVALERYL-COA-DEHYDROGENASE PRECURSOR, IVDH
list all proteins Gene Name GeneID UniProt
IVD 56357 Q9JHI5
IVD 3712 P26440
IVD 24513 P12007

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Isovaleryl-CoA Dehydrogenase Proteins (IVD) by Origin

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Top referenced Isovaleryl-CoA Dehydrogenase Proteins

  1. Human IVD Protein expressed in Escherichia coli (E. coli) - ABIN666949 : Hodges, Galea, Holm, Holm: Corticomotor excitability of back muscles is affected by intervertebral disc lesion in pigs. in The European journal of neuroscience 2009 (PubMed)
    Show all 2 references for ABIN666949

More Proteins for Isovaleryl-CoA Dehydrogenase Interaction Partners

Human Isovaleryl-CoA Dehydrogenase (IVD) interaction partners

  1. Nine novel isovaleryl-CoA dehydrogenase mutations have been found in a Spanish cohort with isovaleric acidemia.

  2. kinetics and ligand binding of isovaleryl-CoA dehydrogenase

  3. A heterogeneous mutation spectrum in the IVD gene was identified in isovaleric acidemia patients in the United Arab Emirates.

  4. A child with isovaleric acidemia was subsequently found to harbour a known missense mutation (c.A1199G [p.Y371C]) and a novel 4-bp duplication (c.1148_1151dupGCTA [p.Y355X]) in the IVD gene. The former may be a founder mutation in the Chinese population.

  5. Replacement of the catalytic glutamate (show GRIN1 Proteins) in either short-chain acyl-CoA dehydrogenase (SCAD (show Acads Proteins)) or isovaleryl-CoA dehydrogenase (IVD)with glycine resulted in a several-fold reduction in affinity for substrate.

  6. Mutations of isovaleryl-CoA dehydrogenase gene is associated with isovaleric acidemia

Arabidopsis thaliana Isovaleryl-CoA Dehydrogenase (IVD) interaction partners

  1. Data elucidates the pathway of plant Lys (show LYZ Proteins) catabolism and demonstrate that both isovaleryl-CoA dehydrogenase and 2-hydroxyglutarate dehydrogenase (show L2HGDH Proteins) act as electron donors to the ubiquinol pool via an ETF (show TEAD2 Proteins)/ETFQO (show ETFDH Proteins)-mediated route. [IVDH]

  2. Accumulation of both homomethionine and 3-isovaleroyloxypropyl-glucosinolate cosegregates with the high branched chain amino acid phenotype in IVD mutants.

Isovaleryl-CoA Dehydrogenase (IVD) Protein Profile

Protein Summary

Isovaleryl-CoA dehydrogenase (IVD) is a mitochondrial matrix enzyme that catalyzes the third step in leucine catabolism. The genetic deficiency of IVD results in an accumulation of isovaleric acid, which is toxic to the central nervous system and leads to isovaleric acidemia. Alternatively spliced transcript variants encoding different isoforms have been found for this gene.

Alternative names and synonyms associated with Isovaleryl-CoA Dehydrogenase (IVD)

  • isovaleryl coenzyme A dehydrogenase (Ivd)
  • isovaleryl-CoA dehydrogenase (IVD)
  • isovaleryl-CoA dehydrogenase (Ivd)
  • isovaleryl-CoA-dehydrogenase (IVD)
  • 1300016K07Rik protein
  • 6720455E18Rik protein
  • ACAD2 protein
  • AI463340 protein
  • ATIVD protein
  • isovaleryl-CoA-dehydrogenase protein
  • IVDH protein

Protein level used designations for IVD

isovaleryl dehydrogenase , isovaleryl-CoA dehydrogenase, mitochondrial , isovaleryl CoA dehydrogenase , isovaleryl Coenzyme A dehydrogenase , isovaleryl coenzyme A dehydrogenase

56357 Mus musculus
3712 Homo sapiens
510440 Bos taurus
24513 Rattus norvegicus
823668 Arabidopsis thaliana
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