NDUFV1 Proteins
The mitochondrial respiratory chain provides energy to cells via oxidative phosphorylation and consists of four membrane-bound electron-transporting protein complexes (I-IV) and an ATP synthase (complex V).
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NADH Dehydrogenase (Ubiquinone) Flavoprotein 1, 51kDa (NDUFV1) (AA 21-464) protein (His tag) Protein
NADH Dehydrogenase (Ubiquinone) Flavoprotein 1, 51kDa (NDUFV1) (AA 21-464) protein (His tag) Protein
NADH Dehydrogenase (Ubiquinone) Flavoprotein 1, 51kDa (NDUFV1) (AA 1-464) protein (GST tag) Protein
NADH Dehydrogenase (Ubiquinone) Flavoprotein 1, 51kDa (NDUFV1) (AA 365-464) protein (GST tag) Protein
NADH Dehydrogenase (Ubiquinone) Flavoprotein 1, 51kDa (NDUFV1) protein (Myc-DYKDDDDK Tag) Protein
NADH Dehydrogenase (Ubiquinone) Flavoprotein 1, 51kDa (NDUFV1) (AA 21-464) protein (His tag) Protein
NADH Dehydrogenase (Ubiquinone) Flavoprotein 1, 51kDa (NDUFV1) (AA 21-464) protein (His tag) Protein
NADH Dehydrogenase (Ubiquinone) Flavoprotein 1, 51kDa (NDUFV1) (AA 21-464) protein (His tag) Protein
NADH Dehydrogenase (Ubiquinone) Flavoprotein 1, 51kDa (NDUFV1) (AA 21-464) protein (His tag) Protein
NDUFV1 Protein Profile
Protein Summary
The mitochondrial respiratory chain provides energy to cells via oxidative phosphorylation and consists of four membrane-bound electron-transporting protein complexes (I-IV) and an ATP synthase (complex V). This gene encodes a 51 kDa subunit of the NADH:ubiquinone oxidoreductase complex I\; a large complex with at least 45 nuclear and mitochondrial encoded subunits that liberates electrons from NADH and channels them to ubiquinone. This subunit carries the NADH-binding site as well as flavin mononucleotide (FMN)- and Fe-S-biding sites. Defects in complex I are a common cause of mitochondrial dysfunction\; a syndrome that occurs in approximately 1 in 10,000 live births. Mitochondrial complex I deficiency is linked to myopathies, encephalomyopathies, and neurodegenerative disorders such as Parkinson's disease and Leigh syndrome. Alternative splicing results in multiple transcript variants encoding distinct isoforms.
Gene names and symbols associated with NDUFV1
- NADH dehydrogenase [ubiquinone] flavoprotein 1, mitochondrial (LOC408367) antibody
- NADH:ubiquinone oxidoreductase core subunit V1 (NDUFV1) antibody
- NADH:ubiquinone oxidoreductase core subunit V1 (ndufv1) antibody
- NADH dehydrogenase ubiquinone flavoprotein 1 (ndufv1) antibody
- NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa (Ndufv1) antibody
- NADH dehydrogenase [ubiquinone] flavoprotein 1, mitochondrial (LOC100179486) antibody
- NADH dehydrogenase (ubiquinone) flavoprotein 1 (ndufv1) antibody
- NADH dehydrogenase (ubiquinone) flavoprotein 1 (Ndufv1) antibody
- NADH:ubiquinone oxidoreductase core subunit V1 (Ndufv1) antibody
- NADH:ubiquinone oxidoreductase core subunit V1 L homeolog (ndufv1.L) antibody
- CI-51K antibody
- CI-51kD antibody
- CI51KD antibody
- DDBDRAFT_0188174 antibody
- DDBDRAFT_0191420 antibody
- DDB_0188174 antibody
- DDB_0191420 antibody
- GB17095 antibody
- UQOR1 antibody
- wu:fc01f01 antibody
- wu:fc12f12 antibody
- zgc:86620 antibody
Protein level used designations for NDUFV1
NADH dehydrogenase [ubiquinone] flavoprotein 1, mitochondrial , NADH dehydrogenase ubiquinone flavoprotein 1 , NADH-ubiquinone oxidoreductase , ubiquinone oxidoreductase , OXPHOS complex I 51 kDa subunit , NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa , NADH dehydrogenase flavoprotein 1; 24 kDa (FP) , NADH-ubiquinone oxidoreductase 51 kDa subunit , complex I-51kD , complex I 51 kda subunit , complex I 51kDa subunit , complex I, mitochondrial respiratory chain , mitochondrial NADH dehydrogenase ubiquinone flavoprotein 1 , mitochondrial NADH:ubiquinone oxidoreductase 51 kda subunit , CI-51kD , NADH dehydrogenase flavoprotein 1 , NADH-ubiquinone oxidoreductase 51 kDa subunit, mitochondrial , mitochondrial complex I subunit NDUFV1
GENE ID | SPECIES |
---|---|
408367 | Apis mellifera |
430210 | Gallus gallus |
496988 | Xenopus (Silurana) tropicalis |
8626872 | Dictyostelium discoideum AX4 |
100122492 | Nasonia vitripennis |
100179486 | Ciona intestinalis |
445291 | Danio rerio |
17995 | Mus musculus |
293655 | Rattus norvegicus |
379907 | Xenopus laevis |
4723 | Homo sapiens |
476004 | Canis lupus familiaris |
287014 | Bos taurus |
747209 | Pan troglodytes |
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