GTP Binding Protein 3 (Mitochondrial) (GTPBP3) ELISA Kits

This locus encodes a GTP-binding protein. Additionally we are shipping GTPBP3 Antibodies (34) and GTPBP3 Proteins (5) and many more products for this protein.

list all ELISA KIts Gene Name GeneID UniProt
GTPBP3 290633 Q5PQQ1
GTPBP3 70359 Q923K4
GTPBP3 84705 Q969Y2
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Catalog No. Reactivity Sensitivity Range Images Quantity Delivery Price Details
  96 Tests 15 to 18 Days
  96 Tests 15 to 18 Days
  96 Tests 15 to 18 Days

More ELISA Kits for GTPBP3 Interaction Partners

Zebrafish GTP Binding Protein 3 (Mitochondrial) (GTPBP3) interaction partners

  1. the Gtpbp3 zebrafish model shows the role of defective nucleotide modifications of tRNAs in mitochondrial biogenesis and suggests pathological consequences in hypertrophic cardiomyopathy

  2. defective expression of gtpbp3 related to tRNA modification alters the mitochondrial function and development of zebrafish

Mouse (Murine) GTP Binding Protein 3 (Mitochondrial) (GTPBP3) interaction partners

  1. These observations suggest that the mouse Gtpbp3 is an evolutionarily conserved mitochondrial GTP-binding protein involved in the tRNA modification.

Human GTP Binding Protein 3 (Mitochondrial) (GTPBP3) interaction partners

  1. Low GTPBP3 expression is associated with Mitochondrial diseases in neoplasms.

  2. Defects in the mitochondrial tRNA modification enzymes MTO1 and GTPBP3 promote different metabolic reprogramming through a HIF-PPARgamma-UCP2-AMPK axis.

  3. GTPBP3 defective expression is associated with an mitochondrial-tRNA hypomodification status.GTPBP3 plays a role in the regulation of UCP2 and MCP1 proteins through AMPK signaling.

  4. Results show that post-transcriptional expression of GTPBP3, MTO1 and TRMU genes is down-regulated, leading to mt-tRNA hypomodification and contributing to mitochondrial dysfunction in MELAS cybrids.

  5. Most individuals with GTPBP3 mutations developed neurological symptoms and MRI involvement of thalamus, putamen, and brainstem resembling Leigh syndrome.

  6. GTPBP3 localizes in the mitochondria and is a deafness-associated homolog of yeast MSS1.

  7. Phenotype of non-syndromic deafness associated with the mitochondrial A1555G mutation is modulated by mitochondrial RNA modifying enzymes MTO1 and GTPBP3.

  8. Data show that the two most abundant GTPBP3 isoforms exhibit moderate affinity for guanine nucleotides like their bacterial homologue, MnmE, although they hydrolyze GTP at a 100-fold lower rate.

GTPBP3 Antigen Profile

Antigen Summary

This locus encodes a GTP-binding protein. The encoded protein is localized to the mitochondria and may play a role in mitochondrial tRNA modification. Polymorphisms at this locus may be associated with severity of aminoglycoside-induced deafness, a disease associated with a mutation in the 12S rRNA. Alternatively spliced transcript variants encoding different isoforms have been described.

Gene names and symbols associated with GTPBP3

  • GTP binding protein 3, mitochondrial (GTPBP3) antibody
  • GTP binding protein 3 (Gtpbp3) antibody
  • GTP binding protein 3, mitochondrial (gtpbp3) antibody
  • 2410009F13Rik antibody
  • AI607903 antibody
  • GTPBG3 antibody
  • GTPBP3 antibody
  • MSS1 antibody
  • MTGP1 antibody
  • THDF1 antibody
  • zgc:112394 antibody

Protein level used designations for GTPBP3

GTP binding protein 3 (mitochondrial) , tRNA modification GTPase GTPBP3, mitochondrial , tRNA modification GTPase GTPBP3, mitochondrial-like , GTP-binding protein 3 , mitochondrial GTP-binding protein 1

484838 Canis lupus familiaris
539656 Bos taurus
100070158 Equus caballus
100392904 Callithrix jacchus
100474937 Ailuropoda melanoleuca
290633 Rattus norvegicus
553807 Danio rerio
70359 Mus musculus
84705 Homo sapiens
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