PEX3 Proteins
The product of PEX3 is involved in peroxisome biosynthesis and integrity.
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Peroxisomal Biogenesis Factor 3 (PEX3) (AA 1-372) protein (rho-1D4 tag) Protein
Peroxisomal Biogenesis Factor 3 (PEX3) (AA 141-372) protein (His tag) Protein
Peroxisomal Biogenesis Factor 3 (PEX3) (AA 141-373) protein (His tag) Protein
Peroxisomal Biogenesis Factor 3 (PEX3) (AA 1-373) protein (rho-1D4 tag) Protein
Peroxisomal Biogenesis Factor 3 (PEX3) (AA 1-373) protein (GST tag) Protein
Peroxisomal Biogenesis Factor 3 (PEX3) (AA 271-373) protein (GST tag) Protein
Peroxisomal Biogenesis Factor 3 (PEX3) (AA 40-441) protein (His tag) Protein
Peroxisomal Biogenesis Factor 3 (PEX3) (AA 34-455) protein (His tag) Protein
PEX3 Protein Profile
Protein Summary
The product of this gene is involved in peroxisome biosynthesis and integrity. It assembles membrane vesicles before the matrix proteins are translocated. Peroxins (PEXs) are proteins that are essential for the assembly of functional peroxisomes. The peroxisome biogenesis disorders (PBDs) are a group of genetically heterogeneous autosomal recessive, lethal diseases characterized by multiple defects in peroxisome function. The peroxisomal biogenesis disorders are a heterogeneous group with at least 14 complementation groups and with more than 1 phenotype being observed in cases falling into particular complementation groups. Although the clinical features of PBD patients vary, cells from all PBD patients exhibit a defect in the import of one or more classes of peroxisomal matrix proteins into the organelle. Defects in this gene are a cause Zellweger syndrome (ZWS).
Gene names and symbols associated with PEX3
- peroxisomal biogenesis factor 3 (LOC692959) antibody
- peroxisomal biogenesis factor 3 (CpipJ_CPIJ013204) antibody
- peroxin 3 (pex3) antibody
- peroxisomal biogenesis factor 3 (PEX3) antibody
- peroxisomal biogenesis factor 3 (pex3) antibody
- peroxisomal biogenesis factor 3 L homeolog (pex3.L) antibody
- peroxisomal biogenesis factor 3 (Pex3) antibody
- 1700014F15Rik antibody
- 2810027F19Rik antibody
- 2900010N04Rik antibody
- DDBDRAFT_0204086 antibody
- DDBDRAFT_0238047 antibody
- DDB_0204086 antibody
- DDB_0238047 antibody
- PBD10A antibody
- Peroxin-3 antibody
- TRG18 antibody
- zgc:56313 antibody
Protein level used designations for PEX3
peroxisomal biogenesis factor 3 , transmembrane protein , peroxin-3 , peroxisomal assembly protein PEX3 , transformation-related protein 18 , Peroxisomal assembly protein PEX3 , peroxisomal assembly protein 3 , Peroxisomal biogenesis factor 3
GENE ID | SPECIES |
---|---|
692959 | Bombyx mori |
6046074 | Culex quinquefasciatus |
8622947 | Dictyostelium discoideum AX4 |
100230879 | Taeniopygia guttata |
100582200 | Nomascus leucogenys |
393197 | Danio rerio |
444067 | Xenopus laevis |
421669 | Gallus gallus |
8504 | Homo sapiens |
484015 | Canis lupus familiaris |
515730 | Bos taurus |
56535 | Mus musculus |
83519 | Rattus norvegicus |
100760471 | Cricetulus griseus |
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