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anti-GDP-Mannose Pyrophosphorylase B (GMPPB) Antibodies

GMPPB is thought to encode a GDP-mannose pyrophosphorylase. Additionally we are shipping GDP-Mannose Pyrophosphorylase B Proteins (9) and and many more products for this protein.

list all antibodies Gene Name GeneID UniProt
GMPPB 29925 Q9Y5P6
GMPPB 331026 Q8BTZ7
GMPPB 363145  
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Top anti-GDP-Mannose Pyrophosphorylase B Antibodies at antibodies-online.com

Showing 10 out of 46 products:

Catalog No. Reactivity Host Conjugate Application Images Quantity Delivery Price Details
Cow Rabbit Un-conjugated WB WB Suggested Anti-Gmppb Antibody Titration: 1.0 ug/ml Positive Control: Mouse Pancreas 100 μL 2 to 3 Days
$319.00
Details
Cow Rabbit Un-conjugated IHC, WB Human kidney 100 μL 2 to 3 Days
$229.00
Details
Cow Rabbit Un-conjugated IHC, IHC (p), WB 100 μL 11 to 14 Days
$493.17
Details
Fruit Fly Rabbit Un-conjugated WB 100 μL 11 to 14 Days
$581.17
Details
Human Mouse Un-conjugated ELISA, IHC, IHC (p), WB 100 μg 11 to 14 Days
$551.83
Details
Human Mouse Un-conjugated IHC (p), ELISA, WB Immunoperoxidase of monoclonal antibody to GMPPB on formalin-fixed paraffin-embedded human adrenal gland. [antibody concentration 3 ug/ml] GMPPB monoclonal antibody (M07), clone 2B5 Western Blot analysis of GMPPB expression in HepG2 . 100 μg 11 to 12 Days
$440.00
Details
Human Rabbit Un-conjugated WB Western Blot at 1:2000 dilution Lane 1: human pancreas lysate Lane 2: mouse pancreas lysate Lysates/proteins at 20 ug per lane. 200 μL 2 to 3 Days
$515.63
Details
Mouse Rabbit Un-conjugated WB Western Blot at 1:4000 dilution + mouse pancreas lysate Lysates/proteins at 20 ug per lane. 200 μL 2 to 3 Days
$515.63
Details
Human Rabbit Un-conjugated IHC, WB GMPPB antibody was used for immunohistochemistry at a concentration of 4-8 ug/ml to stain Epithelial cells of renal tubule (arrows) in Human Kidney. Magnification is at 400X GMPPB antibody was used for immunohistochemistry at a concentration of 4-8 ug/ml. Magnification is at 400X 100 μg 9 to 11 Days
$369.29
Details
Human Rabbit Un-conjugated IHC, ELISA, WB 100 μL 2 to 3 Days
$446.88
Details

More Antibodies against GDP-Mannose Pyrophosphorylase B Interaction Partners

Human GDP-Mannose Pyrophosphorylase B (GMPPB) interaction partners

  1. Data demonstrates that a change in beta-dystroglycan electrophoretic mobility in patients with muscular dystrophy is a distinctive marker of the molecular defect in GMPPB.

  2. Late-onset limb-girdle muscular dystrophy caused by GMPPB mutations.

  3. Study finds that the GMPPB mutation spectrum in Chinese patients may differ from that of European populations, with the mutation p.(Arg357His) most frequently found. These mutations may lead to abnormal folding of GMPPB leading to protein aggregates in the cytoplasm rather than an overall loss in protein expression.

  4. Patients with GMPPB-CMS have phenotypic features aligned with CMS subtypes harbouring mutations within the early stages of the glycosylation pathway. Additional features shared with the dystroglycanopathies include myopathic features, raised Creatine Kinase levels and variable mild cognitive delay.

  5. We observe that c.79G>C (p.D27H) is associated with a mild limb-girdle muscular dystrophy phenotype, whereas c.860G>A (p.R287Q) is associated with a relatively severe congenital muscular dystrophy typically involving brain development.

  6. This study found mutations in GMPPB can lead to a wide spectrum of clinical features where deficit in neuromuscular transmission is the major component in a subset of cases.

  7. The phenotypic spectrum of GMPPB mutations was expanded to include limb-girdle muscular dystrophies.

  8. Work confirms a role for GMPPB defects in alpha-dystroglycanopathy, and suggests that glycosylation may play a role in the neuronal membrane channels or networks involved in the physiology of generalized epilepsy syndromes.

  9. Individuals with GMPPB mutations have hypoglycosylated alpha-dystroglycan in muscle. These mutations cause congenital and limb-girdle muscular dystrophies.

GDP-Mannose Pyrophosphorylase B (GMPPB) Antigen Profile

Protein Summary

This gene is thought to encode a GDP-mannose pyrophosphorylase. The encoded protein catalyzes the conversion of mannose-1-phosphate and GTP to GDP-mannose, a reaction involved in the production of N-linked oligosaccharides. Alternatively spliced transcript variants encoding distinct isoforms have been described.

Gene names and symbols associated with GMPPB

  • GDP-mannose pyrophosphorylase B (gmppb) antibody
  • GDP-mannose pyrophosphorylase B L homeolog (gmppb.L) antibody
  • GDP-mannose pyrophosphorylase B (GMPPB) antibody
  • GDP-mannose pyrophosphorylase B (LOAG_13550) antibody
  • GDP-mannose pyrophosphorylase B (Gmppb) antibody
  • AI317178 antibody
  • E430010H19 antibody
  • GMPPB antibody
  • gmppl antibody
  • MDDGA14 antibody
  • MDDGB14 antibody
  • MDDGC14 antibody
  • RGD1560458 antibody
  • zgc:92026 antibody

Protein level used designations for GMPPB

GTP-mannose-1-phosphate guanylyltransferase beta , mannose-1-phosphate guanyltransferase beta , GDP-mannose pyrophosphorylase B-A , GTP-mannose-1-phosphate guanylyltransferase beta-A , mannose-1-phosphate guanyltransferase beta-A , GDP-mannose pyrophosphorylase B , mannose-1-phosphate guanyltransferase beta-like

GENE ID SPECIES
445097 Danio rerio
447346 Xenopus laevis
100856660 Canis lupus familiaris
460378 Pan troglodytes
493267 Xenopus (Silurana) tropicalis
9951021 Loa loa
100028039 Monodelphis domestica
100357646 Oryctolagus cuniculus
100397938 Callithrix jacchus
100436355 Pongo abelii
100474972 Ailuropoda melanoleuca
100583111 Nomascus leucogenys
29925 Homo sapiens
331026 Mus musculus
514161 Bos taurus
100513376 Sus scrofa
363145 Rattus norvegicus
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