FKRP antibody (C-Term)
Quick Overview for FKRP antibody (C-Term) (ABIN1536611)
Target
See all FKRP AntibodiesReactivity
Host
Clonality
Conjugate
Application
Clone
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Binding Specificity
- AA 418-444, C-Term
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Predicted Reactivity
- M
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Purification
- This antibody is purified through a protein G column, followed by dialysis against PBS.
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Immunogen
- This FKRP antibody is generated from mice immunized with a KLH conjugated synthetic peptide between 418-444 amino acids from the C-terminal region of human FKRP.
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Isotype
- IgG1
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Application Notes
- WB: 1:100
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Restrictions
- For Research Use only
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Format
- Liquid
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Buffer
- Purified monoclonal antibody supplied in PBS with 0.09 % (W/V) sodium azide.
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Preservative
- Sodium azide
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Precaution of Use
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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Storage
- 4 °C,-20 °C
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Storage Comment
- FKRP Antibody (C-term) can be refrigerated at 2-8 °C for up to 6 months. For long term storage, keep at -20 °C.
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Expiry Date
- 6 months
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- FKRP (Fukutin Related Protein (FKRP))
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Alternative Name
- FKRP
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Background
- This gene encodes a protein which is targeted to the medial Golgi apparatus and is necessary for posttranslational modification of dystroglycan. Mutations in this gene have been associated with congenital muscular dystrophy, mental retardation, and cerebellar cysts. Several alternatively spliced transcript variants of this gene have been described, but the full-length nature of some of these variants has not been determined. [provided by RefSeq].
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Molecular Weight
- 54568
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Gene ID
- 79147
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NCBI Accession
- NP_001034974, NP_077277
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UniProt
- Q9H9S5
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Pathways
- Regulation of Carbohydrate Metabolic Process
Target
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