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LRPPRC antibody (AA 1041-1394)
LRPPRC
Reactivity: Human
WB, IHC, IF
Host: Rabbit
Polyclonal
unconjugated
Product Details anti-LRPPRC Antibody
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Target
See all LRPPRC Antibodies
LRPPRC
(Leucine-Rich PPR-Motif Containing (LRPPRC))
Binding Specificity
All epitopes for LRPPRC antibodies
AA 1041-1394
Reactivity
All reactivities for LRPPRC antibodies
Human
Host
All hosts for LRPPRC antibodies
Rabbit
Clonality
All clonalities for LRPPRC antibodies
Polyclonal
Conjugate
All conjugates for LRPPRC antibodies
This LRPPRC antibody is un-conjugated
Application
All applications for LRPPRC antibodies
Western Blotting (WB), Immunohistochemistry (IHC), Immunofluorescence (IF)
Sequence
IACRLNQKKG AYDIFLNAKE QNIVFNAETY SNLIKLLMSE DYFTQAMEVK AFAETHIKGF TLNDAANSRL IITQVRRDYL KEAVTTLKTV LDQQQTPSRL AVTRVIQALA MKGDVENIEV VQKMLNGLED SIGLSKMVFI NNIALAQIKN NNIDAAIENI ENMLTSENKV IEPQYFGLAY LFRKVIEEQL EPAVEKISIM AERLANQFAI YKPVTDFFLQ LVDAGKVDDA RALLQRCGAI AEQTPILLLF LLRNSRKQGK ASTVKSVLEL IPELNEKEEA YNSLMKSYVS EKDVTSAKAL YEHLTAKNTK LDDLFLKRYA SLLKYAGEPV PFIEPPESFE FYAQQLRKLR ENSS
Cross-Reactivity
Human, Mouse, Rat
Characteristics
Polyclonal Antibodies
Immunogen
Recombinant fusion protein containing a sequence corresponding to amino acids 1041-1394 of human LRPPRC (NP_573566.2).
Isotype
IgG
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Alternatives
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Application Details
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Application Notes
WB,1:1000 - 1:2000,IHC,1:100 - 1:200,IF,1:100 - 1:200
Restrictions
For Research Use only
Handling
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Buffer
PBS with 0.02 % sodium azide,50 % glycerol, pH 7.3.
Preservative
Sodium azide
Precaution of Use
This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
Storage
-20 °C
Storage Comment
Store at -20°C. Avoid freeze / thaw cycles.
Target Details for LRPPRC
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Target
LRPPRC
(Leucine-Rich PPR-Motif Containing (LRPPRC))
Alternative Name
LRPPRC (LRPPRC Products )
Background
This gene encodes a leucine-rich protein that has multiple pentatricopeptide repeats (PPR). The precise role of this protein is unknown but studies suggest it may play a role in cytoskeletal organization, vesicular transport, or in transcriptional regulation of both nuclear and mitochondrial genes. The protein localizes primarily to mitochondria and is predicted to have an N-terminal mitochondrial targeting sequence. Mutations in this gene are associated with the French-Canadian type of Leigh syndrome.,LRPPRC,CLONE-23970,GP130,LRP130,LSFC,Epigenetics & Nuclear Signaling,RNA Binding,Endocrine & Metabolism,Mitochondrial metabolism,Neuroscience,Neurodegenerative Diseases,LRPPRC
Molecular Weight
157 kDa
Gene ID
10128
UniProt
P42704
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