Dysferlin antibody (Internal Region)
Quick Overview for Dysferlin antibody (Internal Region) (ABIN5539714)
Target
See all Dysferlin (DYSF) AntibodiesReactivity
Host
Clonality
Conjugate
Application
Grade
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Binding Specificity
- Internal Region
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Purpose
- dysferlin
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Sequence
- HLFCQQHRVK AP
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Specificity
- This antibody is expected to recognize all 14 reported isoforms.
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Cross-Reactivity
- Cow, Human, Pig, Rat
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Purification
- Purified from goat serum by ammonium sulphate precipitation followed by antigen affinity chromatography using the immunizing peptide.
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Isotype
- IgG
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Application Notes
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Western Blot: Preliminary experiments in Human and rodent Heart and Skeletal Muscle lysates gave no specific signal but low background (at antibody concentration up to 1 μg/mL).
Peptide ELISA: antibody detection limit dilution 1:128000.
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Restrictions
- For Research Use only
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Format
- Liquid
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Concentration
- 0.5 mg/mL
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Buffer
- Supplied at 0.5 mg/mL in Tris saline, 0.02 % sodium azide, pH 7.3 with 0.5 % bovine serum albumin.
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Preservative
- Sodium azide
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Precaution of Use
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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Handling Advice
- Minimize freezing and thawing.
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Storage
- -20 °C
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Storage Comment
- Aliquot and store at -20°C, with minimal freeze/thawing. A working aliquot may be refrigerated at 4°C for a few weeks and still remain viable.
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- Dysferlin (DYSF)
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Alternative Name
- DYSF
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Background
- DYSF, dysferlin, limb girdle muscular dystrophy 2B (autosomal recessive), FER1L1, LGMD2B, MMD1, dysferlin, dystrophy-associated fer-1-like 1, dystrophy-associated fer-1-like protein, fer-1-like protein 1
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Gene ID
- 8291, 312492
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NCBI Accession
- NP_001124459, NP_001123927, NP_001124458, NP_001124457, NP_001124456, NP_001124455, NP_001124454, NP_003485, NP_001124448, NP_001124449, NP_001124450, NP_001124451, NP_001124452, NP_001124453
Target
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