This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
Storage
-20 °C
Storage Comment
Aliquot the ACADL antibody and store frozen at -20°C or colder. Avoid repeated freeze-thaw cycles.
Target
ACADL
(Acyl-CoA Dehydrogenase, Long Chain (ACADL))
Alternative Name
ACADL
Background
Long-chain specific acyl-CoA dehydrogenase, mitochondrial belongs to the acyl-CoA dehydrogenase family, which is a family of mitochondrial flavoenzymes involved in fatty acid and branched chain amino-acid metabolism. This protein is one of the four enzymes that catalyze the initial step of mitochondrial beta-oxidation of straight-chain fatty acid. Defects in this gene are the cause of long-chain acyl-CoA dehydrogenase (LCAD) deficiency, leading to nonketotic hypoglycemia.