FKRP antibody (AA 30-220)

Catalog No. ABIN6140666

The Rabbit Polyclonal anti-FKRP antibody has been validated for WB and IHC. It is suitable to detect FKRP in samples from Human.

Quick Overview for FKRP antibody (AA 30-220) (ABIN6140666)

Target: FKRP (Fukutin Related Protein (FKRP))

Reactivity: Human

Host: Rabbit

Clonality: Polyclonal

Conjugate: This FKRP antibody is un-conjugated

Application: Western Blotting (WB), Immunohistochemistry (IHC)

Product Details anti-FKRP Antibody

Binding Specificity: AA 30-220

Sequence: QPRNSRARGP RRASAAGPRV TVLVREFEAF DNAVPELVDS FLQQDPAQPV VVAADTLPYP PLALPRIPNV RLALLQPALD RPAAASRPET YVATEFVALV PDGARAEAPG LLERMVEALR AGSARLVAAP VATANPARCL ALNVSLREWT ARYGAAPAAP RCDALDGDAV VLLRARDLFN LSAPLARPVG T

Cross-Reactivity: Human, Mouse, Rat

Characteristics: Polyclonal Antibodies

Purification: Affinity purification

Immunogen: Recombinant fusion protein containing a sequence corresponding to amino acids 30-220 of human FKRP (NP_077277.1).

Isotype: IgG

Application Details

Application Notes: WB,1:1000 - 1:3000,IHC,1:50 - 1:200

Comment:

HIGH QUALITY

Restrictions: For Research Use only

Handling

Format: Liquid

Buffer: PBS with 0.02 % sodium azide,50 % glycerol, pH 7.3.

Preservative: Sodium azide

Precaution of Use: This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Storage: -20 °C

Storage Comment: Store at -20°C. Avoid freeze / thaw cycles.

Target Details for FKRP

Target: FKRP (Fukutin Related Protein (FKRP))

Alternative Name: FKRP

Background: This gene encodes a protein which is targeted to the medial Golgi apparatus and is necessary for posttranslational modification of dystroglycan. Mutations in this gene have been associated with congenital muscular dystrophy, mental retardation, and cerebellar cysts. Several alternatively spliced transcript variants of this gene have been described, but the full-length nature of some of these variants has not been determined.,FKRP,LGMD2I,MDC1C,MDDGA5,MDDGB5,MDDGC5,Signal Transduction,FKRP

Molecular Weight: 54 kDa

Gene ID: 79147

UniProt: Q9H9S5

Pathways: Regulation of Carbohydrate Metabolic Process