ASS1 antibody
Quick Overview for ASS1 antibody (ABIN7245992)
Target
See all ASS1 AntibodiesReactivity
Host
Clonality
Conjugate
Application
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Characteristics
- Polyclonal Antibody
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Purification
- Antigen affinity purification
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Immunogen
- Fusion protein of human ASS1
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Isotype
- IgG
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Application Notes
- WB 1:500-1:2000, IHC 1:25-1:100, ELISA 1:5000-1:10000
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Restrictions
- For Research Use only
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Format
- Liquid
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Concentration
- 0.5 mg/mL
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Buffer
- PBS with 0.05 % Sodium azide and 40 % Glycerol, pH 7.4
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Preservative
- Sodium azide
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Precaution of Use
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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Storage
- -20 °C
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Storage Comment
- Store at -20°C. Avoid freeze / thaw cycles.
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- ASS1 (Argininosuccinate Synthase 1 (ASS1))
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Alternative Name
- ASS1
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Background
- ASS1 is a rate-limiting enzyme in the urea cycle. Citrullinemia type I is an autosomal recessive disorder that is caused by a deficiency of the urea cycle enzyme argininosuccinate synthetase (ASS1). Deficiency of ASS1 shows various clinical manifestations encompassing severely affected patients with fatal neonatal hyperammonemia as well as asymptomatic individuals with only a biochemical phenotype.
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Molecular Weight
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Observed_MW: Refer to figures
Calculated_MW: 47 kDa
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UniProt
- P00966
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Pathways
- Response to Growth Hormone Stimulus, Cellular Response to Molecule of Bacterial Origin
Target
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