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Dysferlin antibody (AA 105-278)

The Rabbit Polyclonal anti-Dysferlin antibody has been validated for ELISA, IHC and IF. It is suitable to detect Dysferlin in samples from Human.
Catalog No. ABIN7150914

Quick Overview for Dysferlin antibody (AA 105-278) (ABIN7150914)

Target

See all Dysferlin (DYSF) Antibodies
Dysferlin (DYSF)

Reactivity

  • 59
  • 25
  • 5
  • 4
  • 4
  • 4
  • 4
  • 2
  • 2
  • 2
  • 2
Human

Host

  • 53
  • 5
  • 1
Rabbit

Clonality

  • 46
  • 13
Polyclonal

Conjugate

  • 26
  • 4
  • 3
  • 2
  • 2
  • 2
  • 2
  • 2
  • 2
  • 2
  • 1
  • 1
  • 1
  • 1
  • 1
  • 1
  • 1
  • 1
  • 1
  • 1
  • 1
  • 1
This Dysferlin antibody is un-conjugated

Application

  • 20
  • 16
  • 15
  • 14
  • 8
  • 7
  • 5
  • 2
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  • 1
  • 1
ELISA, Immunohistochemistry (IHC), Immunofluorescence (IF)
  • Binding Specificity

    • 16
    • 6
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    • 2
    • 2
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    AA 105-278

    Cross-Reactivity

    Human

    Purification

    >95%, Protein G purified

    Immunogen

    Recombinant Human Dysferlin protein (105-278AA)

    Isotype

    IgG
  • Application Notes

    Recommended dilution: IHC:1:20-1:200, IF:1:50-1:200,

    Restrictions

    For Research Use only
  • Format

    Liquid

    Buffer

    Preservative: 0.03 % Proclin 300
    Constituents: 50 % Glycerol, 0.01M PBS, pH 7.4

    Preservative

    ProClin

    Precaution of Use

    This product contains ProClin: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

    Storage

    -20 °C,-80 °C

    Storage Comment

    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • Target

    Dysferlin (DYSF)

    Alternative Name

    DYSF

    Background

    Background: Key calcium ion sensor involved in the Ca(2+)-triggered synaptic vesicle-plasma membrane fusion. Plays a role in the sarcolemma repair mechanism of both skeletal muscle and cardiomyocytes that permits rapid resealing of membranes disrupted by mechanical stress (By similarity).

    Aliases: DMAT antibody, DYSF antibody, DYSF_HUMAN antibody, Dysferlin antibody, Dysferlin limb girdle muscular dystrophy 2B (autosomal recessive) antibody, Dysferlin limb girdle muscular dystrophy 2B antibody, Dystrophy associated fer 1 like 1 antibody, Dystrophy associated fer 1 like protein antibody, Dystrophy associated fer1 like 1 antibody, Dystrophy associated fer1 like protein antibody, Dystrophy-associated fer-1-like protein antibody, Fer 1 like protein 1 antibody, Fer-1-like protein 1 antibody, Fer1 like protein 1 antibody, FER1L1 antibody, FLJ00175 antibody, FLJ90168 antibody, LGMD 2B antibody, LGMD2B antibody, Limb girdle muscular dystrophy 2B (autosomal recessive) antibody, Limb girdle muscular dystrophy 2B antibody, Miyoshi myopathy antibody, MM antibody, MMD1 antibody

    UniProt

    O75923
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