Dysferlin antibody (AA 105-278)
Quick Overview for Dysferlin antibody (AA 105-278) (ABIN7150914)
Target
See all Dysferlin (DYSF) AntibodiesReactivity
Host
Clonality
Conjugate
Application
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Binding Specificity
- AA 105-278
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Cross-Reactivity
- Human
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Purification
- >95%, Protein G purified
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Immunogen
- Recombinant Human Dysferlin protein (105-278AA)
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Isotype
- IgG
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Application Notes
- Recommended dilution: IHC:1:20-1:200, IF:1:50-1:200,
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Restrictions
- For Research Use only
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Format
- Liquid
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Buffer
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Preservative: 0.03 % Proclin 300
Constituents: 50 % Glycerol, 0.01M PBS, pH 7.4 -
Preservative
- ProClin
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Precaution of Use
- This product contains ProClin: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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Storage
- -20 °C,-80 °C
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Storage Comment
- Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
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- Dysferlin (DYSF)
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Alternative Name
- DYSF
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Background
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Background: Key calcium ion sensor involved in the Ca(2+)-triggered synaptic vesicle-plasma membrane fusion. Plays a role in the sarcolemma repair mechanism of both skeletal muscle and cardiomyocytes that permits rapid resealing of membranes disrupted by mechanical stress (By similarity).
Aliases: DMAT antibody, DYSF antibody, DYSF_HUMAN antibody, Dysferlin antibody, Dysferlin limb girdle muscular dystrophy 2B (autosomal recessive) antibody, Dysferlin limb girdle muscular dystrophy 2B antibody, Dystrophy associated fer 1 like 1 antibody, Dystrophy associated fer 1 like protein antibody, Dystrophy associated fer1 like 1 antibody, Dystrophy associated fer1 like protein antibody, Dystrophy-associated fer-1-like protein antibody, Fer 1 like protein 1 antibody, Fer-1-like protein 1 antibody, Fer1 like protein 1 antibody, FER1L1 antibody, FLJ00175 antibody, FLJ90168 antibody, LGMD 2B antibody, LGMD2B antibody, Limb girdle muscular dystrophy 2B (autosomal recessive) antibody, Limb girdle muscular dystrophy 2B antibody, Miyoshi myopathy antibody, MM antibody, MMD1 antibody
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UniProt
- O75923
Target
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