FH antibody (AA 411-510) (Biotin)
Quick Overview for FH antibody (AA 411-510) (Biotin) (ABIN751425)
Target
See all FH AntibodiesReactivity
Host
Clonality
Conjugate
Application
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Binding Specificity
- AA 411-510
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Predicted Reactivity
- Human,Mouse,Rat,Dog,Cow,Sheep,Pig,Horse,Rabbit
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Purification
- Purified by Protein A.
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Immunogen
- KLH conjugated synthetic peptide derived from human Fumarate hydratase (447-496aa)
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Isotype
- IgG
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Application Notes
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IHC-P 1:200-400
IHC-F 1:100-500 -
Restrictions
- For Research Use only
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Format
- Liquid
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Concentration
- 1 μg/μL
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Buffer
- Aqueous buffered solution containing 0.01M TBS ( pH 7.4) with 1 % BSA, 0.03 % Proclin300 and 50 % Glycerol.
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Preservative
- ProClin
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Precaution of Use
- This product contains ProClin: a POISONOUS AND HAZARDOUS SUBSTANCE, which should be handled by trained staff only.
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Storage
- -20 °C
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Storage Comment
- Store at -20°C for 12 months.
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Expiry Date
- 12 months
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- FH (Fumarate Hydratase (FH))
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Alternative Name
- Fumarate hydratase/FH
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Background
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Synonyms: mitochondrial, FH, Fumarase, Fumarate hydratase, Fumarate hydratase mitochondrial, FUMH_HUMAN, HLRCC, LRCC, MCL, MCUL 1, MCUL1, Multiple hereditary cutaneous leiomyomata.
Background: Defects in FH are the cause of fumarase deficiency (FHD)also known as fumaricaciduria. FHD is characterized by progressive encephalopathy, developmental delay, hypotonia, cerebral atrophy and lactic and pyruvic acidemia.
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Gene ID
- 2271
Target
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