Glucosidase, Alpha, Acid (GAA) Peptide
Quick Overview for Glucosidase, Alpha, Acid (GAA) Peptide (ABIN938303)
Target
Origin
Source
Application
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Peptide Type
- Synthetic
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Sequence
- FGVIVRRQLD GRVLLNTTVA PLFFADQFLQ LSTSLPSQYI TGLAEHLSPL
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Characteristics
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A synthetic peptide for use as a blocking control in assays to test for specificity of GAA antibody,
Alternative Names: GAA control peptide, GAA antibody Blocking Peptide, Anti-GAA Blocking Peptide, Glucosidase Alpha, Acid Blocking Peptide, LYAG Blocking Peptide
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Application Notes
- Optimal conditions should be determined by the investigator
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Restrictions
- For Research Use only
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Format
- Lyophilized
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Reconstitution
- Add 100 µL of distilled water for a final peptide concentration is 1 mg/mL.
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Buffer
- PBS
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Handling Advice
- Avoid repeated freeze/thaw cycles.
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Storage
- -20 °C
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Storage Comment
- Store at -20 °C long term.
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- GAA (Glucosidase, Alpha, Acid (GAA))
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Background
- GAA is acid alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes. Different forms of acid alpha-glucosidase are obtained by proteolytic processing. Defects in this gene are the cause of glycogen storage disease II, also known as Pompe's disease, which is an autosomal recessive disorder with a broad clinical spectrum.
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Molecular Weight
- 98 kDa
Target
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