Glucosidase, Alpha, Acid (GAA) Peptide
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- Target See all GAA products
- GAA (Glucosidase, Alpha, Acid (GAA))
- Peptide Type
- Synthetic
- Origin
- Mammalian
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Source
- Synthetic
- Application
- Blocking Peptide (BP), Immunohistochemistry (IHC), Western Blotting (WB)
- Sequence
- FGVIVRRQLD GRVLLNTTVA PLFFADQFLQ LSTSLPSQYI TGLAEHLSPL
- Characteristics
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A synthetic peptide for use as a blocking control in assays to test for specificity of GAA antibody,
Alternative Names: GAA control peptide, GAA antibody Blocking Peptide, Anti-GAA Blocking Peptide, Glucosidase Alpha, Acid Blocking Peptide, LYAG Blocking Peptide
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- Application Notes
- Optimal conditions should be determined by the investigator
- Restrictions
- For Research Use only
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- Format
- Lyophilized
- Reconstitution
- Add 100 µL of distilled water for a final peptide concentration is 1 mg/mL.
- Buffer
- PBS
- Handling Advice
- Avoid repeated freeze/thaw cycles.
- Storage
- -20 °C
- Storage Comment
- Store at -20 °C long term.
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- Target
- GAA (Glucosidase, Alpha, Acid (GAA))
- Background
- GAA is acid alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes. Different forms of acid alpha-glucosidase are obtained by proteolytic processing. Defects in this gene are the cause of glycogen storage disease II, also known as Pompe's disease, which is an autosomal recessive disorder with a broad clinical spectrum.
- Molecular Weight
- 98 kDa
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