Optimal working dilution should be determined by the investigator.
Restrictions
For Research Use only
Reconstitution
Add 50 μL of distilled water to a final concentration of 1 mg/mL.
Handling Advice
Avoid repeated freezing and thawing.
Storage
4 °C/-20 °C
Storage Comment
Store lyophilized at 2-8 °C or at -20 °C long term. After reconstitution store the antibody undiluted at 2-8 °C for up to one month or in aliquots at -20 °C long term.
Target
ACADL
(Acyl-CoA Dehydrogenase, Long Chain (ACADL))
zgc:55656 antibody, ACAD4 antibody, LCAD antibody, ACOADA antibody, AA960361 antibody, AU018452 antibody, C79855 antibody, acyl-CoA dehydrogenase long chain antibody, acyl-CoA dehydrogenase, long chain antibody, acyl-CoA dehydrogenase, long chain L homeolog antibody, acyl-Coenzyme A dehydrogenase, long-chain antibody, acadl antibody, ACADL antibody, Acadl antibody, acadl.L antibody
Background
ACADL belongs to the acyl-CoA dehydrogenase family, which is a family of mitochondrial flavoenzymes involved in fatty acid and branched chain amino-acid metabolism. This protein is one of the four enzymes that catalyze the initial step of mitochondrial beta-oxidation of straight-chain fatty acid. Defects in ACADL gene are the cause of long-chain acyl-CoA dehydrogenase (LCAD) deficiency, leading to nonketotic hypoglycemia.The protein encoded by this gene belongs to the acyl-CoA dehydrogenase family, which is a family of mitochondrial flavoenzymes involved in fatty acid and branched chain amino-acid metabolism. This protein is one of the four enzymes that catalyze the initial step of mitochondrial beta-oxidation of straight-chain fatty acid. Defects in this gene are the cause of long-chain acyl-CoA dehydrogenase (LCAD) deficiency, leading to nonketotic hypoglycemia.Synonyms: LCAD, Long-chain specific acyl-CoA dehydrogenase, mitochondrial