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P5CS antibody (C-Term)
ALDH18A1
Reactivity: Human, Mouse, Rat, Cow, Pig, Dog
WB, EIA
Host: Goat
Polyclonal
unconjugated
Product Details anti-P5CS Antibody
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Target
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P5CS (ALDH18A1)
(Aldehyde Dehydrogenase 18 Family, Member A1 (ALDH18A1))
Binding Specificity
All epitopes for P5CS antibodies
C-Term
Reactivity
All reactivities for P5CS antibodies
Human, Mouse, Rat, Cow, Pig, Dog
Host
All hosts for P5CS antibodies
Goat
Clonality
All clonalities for P5CS antibodies
Polyclonal
Conjugate
All conjugates for P5CS antibodies
This P5CS antibody is un-conjugated
Application
All applications for P5CS antibodies
Western Blotting (WB), Enzyme Immunoassay (EIA)
Sequence
C-SEHGSLKYLH
Specificity
This antibody is expected to recognize both reported isoforms of ALDH18A1 (NP_002851.2, NP_001017423.1).
Cross-Reactivity (Details)
Species reactivity (expected):Rat, Canine (Dog), Cow, Pig. Species reactivity (tested):Human, Mouse.
Purification
Ammonium Sulphate Precipitation followed by Antigen Affinity Chromatography using the immunizing peptide.
Immunogen
Peptide with sequence from the C Terminus of the protein sequence according to NP_002851.2, NP_001017423.1. Genename: ALDH18A1
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Discover our top product ALDH18A1 Primary Antibody
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Application Details
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Application Notes
Optimal working dilution should be determined by the investigator.
Restrictions
For Research Use only
Handling
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Concentration
0.5 mg/mL
Buffer
Tris saline, pH 7.3 containing 0.02 % Sodium Azide as preservative and 0.5 % BSA as stabilizer.
Preservative
Sodium azide
Precaution of Use
This product contains sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
Handling Advice
Avoid repeated freezing and thawing.
Storage
4 °C/-20 °C
Storage Comment
Store the antibody undiluted at 2-8 °C for one month or (in aliquots) at -20 °C for longer.
Target Details for P5CS
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Target
P5CS (ALDH18A1)
(Aldehyde Dehydrogenase 18 Family, Member A1 (ALDH18A1))
Alternative Name
ALDH18A1 (ALDH18A1 Products )
Synonyms
ALDH18A1 antibody, ARCL3A antibody, GSAS antibody, P5CS antibody, PYCS antibody, 2810433K04Rik antibody, AI429789 antibody, Pycs antibody, cb842 antibody, cb899 antibody, pycs antibody, sb:cb881 antibody, wu:fa91f10 antibody, wu:fi05f11 antibody, wu:fi17d12 antibody, aldehyde dehydrogenase 18 family member A1 antibody, aldehyde dehydrogenase 18 family, member A1 antibody, aldehyde dehydrogenase 18 family member A1 L homeolog antibody, ALDH18A1 antibody, aldh18a1 antibody, Aldh18a1 antibody, aldh18a1.L antibody
Background
Defects in ALDH18A1 are the cause of mental retardation-joint hypermobility-skin laxity with or without metabolic abnormalities (MRJHSL) [MIM:612652]. Clinical manifestations include microcephaly, progressive neurologic dysfunction, mental retardation, progeroid appearance, joint hypermobility, skin laxity and hyperelasticity, cataracts. Some patients manifest metabolic disturbances such as hyperammonemia, hypoornithinemia, hypocitrullinemia, hypoargininemia and hypoprolinemia.Synonyms: Aldehyde dehydrogenase family 18 member A1, Delta-1-pyrroline-5-carboxylate synthetase, GSAS, P5CS, PYCS
Molecular Weight
87.3kDa (NP_002851.2).
Gene ID
5832
NCBI Accession
NP_001017423
UniProt
P54886
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