Browse our Enoyl CoA Hydratase, Short Chain, 1, Mitochondrial (ECHS1) ELISA Kits

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Enoyl CoA Hydratase, Short Chain, 1, Mitochondrial ELISA Kits (ECHS1)
On www.antibodies-online.com are 5 Enoyl CoA Hydratase, Short Chain, 1, Mitochondrial (ECHS1) ELISA Kits from 2 different suppliers available. Additionally we are shipping Enoyl CoA Hydratase, Short Chain, 1, Mitochondrial Antibodies (61) and Enoyl CoA Hydratase, Short Chain, 1, Mitochondrial Proteins (15) and many more products for this protein. A total of 90 Enoyl CoA Hydratase, Short Chain, 1, Mitochondrial products are currently listed.
Synonyms:
C80529, cOR6not, fj55e05, SCEH, si:zc217g15.1, wu:fj55e05
list all ELISA KIts Gene Name GeneID UniProt
ECHS1 1892 P30084
ECHS1 140547 P14604
ECHS1 93747 Q8BH95

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Enoyl CoA Hydratase, Short Chain, 1, Mitochondrial (ECHS1) ELISA Kits by Reactivity

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More ELISA Kits for Enoyl CoA Hydratase, Short Chain, 1, Mitochondrial Interaction Partners

Human Enoyl CoA Hydratase, Short Chain, 1, Mitochondrial (ECHS1) interaction partners

  1. Whole exome sequencing identified heterozygous ECHS1 mutations c.836T>C (novel) and c.8C>A for short-chain enoyl-CoA hydratase (SCEH) deficiency of which 1/2 of the cases are associated with secondary lymphocyte pyruvate dehydrogenase (show PDP ELISA Kits) complex deficiency.[review]

  2. This is the first report of homozygosity for a truncating mutation in ECHS1, which may explain the severe phenotype. Our report highlights the need to consider SCEH deficiency in patients with lethal neonatal lactic acidosis

  3. Human ECHS1 catalyses the hydration of five substrates via different metabolic pathways, with the highest specificity for crotonyl-CoA and the lowest specificity for tiglyl-CoA

  4. These results suggested that ECHS1 may promote cell proliferation in hepatocellular carcinoma in an EGFR (show EGFR ELISA Kits)-dependent manner.

  5. In conclusion, the results of the present study suggested that ECHS1 may have an important role in colorectal cancer cell proliferation and migration

  6. identification of four additional patients with mutations in ECHS1 highlights the importance of the valine degradation pathway in Leigh syndrome

  7. ECHS1 mutations cause combined respiratory chain deficiency resulting in Leigh syndrome.

  8. ECHS1 may play important roles in gastric cancer cell proliferation and migration through PKB (show AKT1 ELISA Kits)- and GSK3b (show GSK3b ELISA Kits)-related signaling pathways.

  9. The study demonstrated that ECHS1 mutations result in ECHS1 deficiency and are another cause of Leigh disease in two siblings.

  10. ECHS1 knockdown reduced cell viability and enhanced cisplatin-induced apoptosis in hepatocellular carcinoma cells.

Mouse (Murine) Enoyl CoA Hydratase, Short Chain, 1, Mitochondrial (ECHS1) interaction partners

  1. potential protein targets for the loss of PostC may include F(1)-ATPase (show DNAH8 ELISA Kits) gamma, Echs1 and Hsp20 (show HSPB6 ELISA Kits) that could regulate cellular ATP consumption/production and defense response to ischaemic stress

Enoyl CoA Hydratase, Short Chain, 1, Mitochondrial (ECHS1) Antigen Profile

Antigen Summary

The protein encoded by this gene functions in the second step of the mitochondrial fatty acid beta-oxidation pathway. It catalyzes the hydration of 2-trans-enoyl-coenzyme A (CoA) intermediates to L-3-hydroxyacyl-CoAs. The gene product is a member of the hydratase/isomerase superfamily. It localizes to the mitochondrial matrix. Transcript variants utilizing alternative transcription initiation sites have been described in the literature.

Alternative names and synonyms associated with Enoyl CoA Hydratase, Short Chain, 1, Mitochondrial (ECHS1)

  • enoyl CoA hydratase, short chain, 1, mitochondrial (echs1) Elisa Kit
  • enoyl CoA hydratase, short chain, 1, mitochondrial (ECHS1) Elisa Kit
  • enoyl CoA hydratase, short chain, 1, mitochondrial (Echs1) Elisa Kit
  • enoyl Coenzyme A hydratase, short chain, 1, mitochondrial (echs1) Elisa Kit
  • enoyl Coenzyme A hydratase, short chain, 1, mitochondrial (Echs1) Elisa Kit
  • C80529 Elisa Kit
  • cOR6not Elisa Kit
  • fj55e05 Elisa Kit
  • SCEH Elisa Kit
  • si:zc217g15.1 Elisa Kit
  • wu:fj55e05 Elisa Kit

Protein level used designations for ECHS1

enoyl Coenzyme A hydratase, short chain, 1, mitochondrial , enoyl-CoA hydratase 1 , enoyl-CoA hydratase, mitochondrial , short-chain enoyl-CoA hydratase , SCEH , short chain enoyl-CoA hydratase , Enoyl-CoA hydratase short chain 1 mitochondrial , Enoyl-CoA hydratase, short chain 1, mitochondrial , enoyl Coenzyme A hydratase, short chain 1 , mitochondrial short-chain enoyl-coenzyme A hydratase 1

GENE ID SPECIES
733431 Xenopus laevis
1892 Homo sapiens
480828 Canis lupus familiaris
100156927 Sus scrofa
281748 Bos taurus
140547 Rattus norvegicus
770828 Gallus gallus
368912 Danio rerio
93747 Mus musculus
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