FKRP antibody (AA 1-50)

Catalog No. ABIN1534132

The Rabbit Polyclonal anti-FKRP antibody is suitable to detect FKRP in samples from Human, Mouse and Rat. It has been validated for WB, ELISA and IF.

Quick Overview for FKRP antibody (AA 1-50) (ABIN1534132)

Target: FKRP (Fukutin Related Protein (FKRP))

Reactivity: Human, Mouse, Rat

Host: Rabbit

Clonality: Polyclonal

Conjugate: This FKRP antibody is un-conjugated

Application: Western Blotting (WB), ELISA, Immunofluorescence (IF)

Product Details anti-FKRP Antibody

Binding Specificity: AA 1-50

Purpose: FKRP Antibody

Specificity: FKRP Polyclonal Antibody detects endogenous levels of FKRP protein.

Purification: The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen.

Purity: > 95 %

Immunogen: The antiserum was produced against synthesized peptide derived from human FKRP. AA range:1-50

Isotype: IgG

Application Details

Application Notes: WB 1:500 - 1:2000. IF 1:200 - 1:1000. ELISA: 1:20000. Not yet tested in other applications.

Restrictions: For Research Use only

Handling

Format: Liquid

Concentration: 1 mg/mL

Buffer: Liquid in PBS containing 50 % glycerol, 0.5 % BSA and 0.02 % sodium azide.

Preservative: Sodium azide

Precaution of Use: This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Storage: -20 °C

Storage Comment: Store at -20°C/1 year

Expiry Date: 12 months

Target Details for FKRP

Target: FKRP (Fukutin Related Protein (FKRP))

Alternative Name: FKRP

Background:

Synonyms: FKRP, Fukutin-related protein

Background: This gene encodes a protein which is targeted to the medial Golgi apparatus and is necessary for posttranslational modification of dystroglycan. Mutations in this gene have been associated with congenital muscular dystrophy, mental retardation, and cerebellar cysts. Several alternatively spliced transcript variants of this gene have been described, but the full-length nature of some of these variants has not been determined. [provided by RefSeq, Oct 2008],

Gene Name: FKRP

Protein Name: Fukutin-related protein

Molecular Weight: 54 kDa

Gene ID: 79147

OMIM: 236670

UniProt: Q9H9S5

Pathways: Regulation of Carbohydrate Metabolic Process