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SGSH antibody (AA 44-200)
SGSH
Reactivity: Human
WB
Host: Rabbit
Polyclonal
unconjugated
Product Details anti-SGSH Antibody
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Target
See all SGSH Antibodies
SGSH
(N-Sulfoglucosamine Sulfohydrolase (SGSH))
Binding Specificity
All epitopes for SGSH antibodies
AA 44-200
Reactivity
All reactivities for SGSH antibodies
Human
Host
All hosts for SGSH antibodies
Rabbit
Clonality
All clonalities for SGSH antibodies
Polyclonal
Conjugate
All conjugates for SGSH antibodies
This SGSH antibody is un-conjugated
Application
All applications for SGSH antibodies
Western Blotting (WB)
Purification
Affinity purified by Protein A.
Immunogen
Recombinant protein fragment contain a sequence corresponding to a region within amino acids 44 and 200 of Human SGSH
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Alternatives
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Application Details
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Application Notes
Suggested dilutions: Western blotting: 1.500-1.3000
Restrictions
For Research Use only
Handling
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Format
Liquid
Buffer
0.1 M Tris-buffered saline with 10 % Glycerol (pH 7.0).0.01 % Thimerosal was added as a preservative.
Preservative
Thimerosal (Merthiolate)
Precaution of Use
Biohazard Informations: This product contains thimerosal which is hazardous.
Storage
4 °C/-20 °C
Storage Comment
Store at -20 °C for long term preservation (recommended). Store at 4 °C for short term use.
Target Details for SGSH
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Target
SGSH
(N-Sulfoglucosamine Sulfohydrolase (SGSH))
Alternative Name
SGSH (SGSH Products )
Synonyms
HSS antibody, MPS3A antibody, SFMD antibody, 4632406A19Rik antibody, N-sulfoglucosamine sulfohydrolase antibody, N-sulfoglucosamine sulfohydrolase (sulfamidase) antibody, SGSH antibody, Sgsh antibody
Background
This gene encodes one of several enzymes involved in the lysosomal degradation of heparan sulfate.Mutations in this gene are associated with Sanfilippo syndrome A, one type of the lysosomal storage disease mucopolysaccaridosis III, which results from impaired degradation of heparan sulfate.Transcripts of varying sizes have been reported but their biological validity has not been determined.[provided by RefSeq]
Molecular Weight
57 kDa
Gene ID
6448
NCBI Accession
NM_000199 , NP_000190
Pathways
Glycosaminoglycan Metabolic Process
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