ETFDH
Reactivity: Human
Host: Rabbit
Polyclonal
FITC
Application Notes
Western blot: 1: 100 - 1: 500. ELISA: 1: 1,000. Other applications not tested. Optimal dilutions are dependent on conditions and should be determined by the user.
Restrictions
For Research Use only
Format
Liquid
Concentration
0.25 mg/mL
Buffer
PBS with 0.09 % (W/V) sodium azide
Preservative
Sodium azide
Precaution of Use
This product contains sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
Handling Advice
Avoid repeated freezing and thawing.
Storage
4 °C/-20 °C
Storage Comment
Store the antibody at 2 - 8 °C up to one month or (in aliquots) at -20 °C for longer.
ETFQO antibody, MADD antibody, 0610010I20Rik antibody, AV001013 antibody, MGC81928 antibody, zgc:92093 antibody, wu:fa05a11 antibody, wu:fb71g06 antibody, MGC69479 antibody, DDBDRAFT_0206234 antibody, DDBDRAFT_0267019 antibody, DDB_0206234 antibody, DDB_0267019 antibody, ETF-QO antibody, electron transfer flavoprotein dehydrogenase antibody, electron transferring flavoprotein, dehydrogenase antibody, electron transfer flavoprotein dehydrogenase L homeolog antibody, electron-transferring-flavoprotein dehydrogenase antibody, electron transfer flavoprotein-ubiquinone oxidoreductase antibody, Electron-transferring-flavoprotein dehydrogenase antibody, ETFDH antibody, Etfdh antibody, etfdh.L antibody, etfdh antibody, CBU_1120 antibody, ZMO1184 antibody, RPE_4421 antibody, Daci_4310 antibody, Bphyt_2765 antibody, Dtpsy_1751 antibody, Za10_0145 antibody, Mesop_5359 antibody
Background
Electron-transferring-flavoprotein dehydrogenase in the inner mitochondrial membrane accepts electrons from electron-transfer flavoprotein which is located in the mitochondrial matrix and reduces ubiquinone in the mitochondrial membrane. The protein is synthesized as a 67- kDa precursor which is targeted to mitochondria and processed in a single step to a 64- kDa mature form located in the mitochondrial membrane. Deficiency in electron-transferring-flavoprotein dehydrogenase have been demonstrated in some patients with type II glutaricacidemia.Synonyms: ETF-QO, ETF-ubiquinone oxidoreductase, Electron transfer flavoprotein-ubiquinone oxidoreductase