Peroxisomal Bifunctional Enzyme antibody (Middle Region)
ECHP
Reactivity: Human
WB
Host: Rabbit
Polyclonal
unconjugated
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- Target See all Peroxisomal Bifunctional Enzyme (ECHP) products
- Peroxisomal Bifunctional Enzyme (ECHP)
- Binding Specificity
- Middle Region
- Reactivity
- Human
- Host
- Rabbit
- Clonality
- Polyclonal
- Application
- Western Blotting (WB)
- Sequence
- VIAVDSDKNQ LATANKMITS VLEKEASKMQ QSGHPWSGPK PRLTSSVKEL
- Characteristics
- This is a rabbit polyclonal antibody against ECHP. It was validated on Western Blot.
- Purification
- Affinity purified
- Immunogen
- The immunogen is a synthetic peptide directed towards the middle region of Human ECHP
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- Application Notes
- Optimal working dilution should be determined by the investigator.
- Restrictions
- For Research Use only
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- Format
- Liquid
- Buffer
- Liquid. Purified antibody supplied in 1x PBS buffer with 0.09 % (w/v) sodium azide and 2 % sucrose.
- Preservative
- Sodium azide
- Precaution of Use
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
- Storage
- -20 °C
- Storage Comment
- For short term use, store at 2-8°C up to 1 week. For long term storage, store at -20°C in small aliquots to prevent freeze-thaw cycles.
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- Target
- Peroxisomal Bifunctional Enzyme (ECHP)
- Alternative Name
- ECHP (ECHP Products)
- Background
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The protein encoded by this gene is a bifunctional enzyme and is one of the four enzymes of the peroxisomal beta-oxidation pathway. The N-terminal region of the encoded protein contains enoyl-CoA hydratase activity while the C-terminal region contains 3-hydroxyacyl-CoA dehydrogenase activity. Defects in this gene are a cause of peroxisomal disorders such as Zellweger syndrome. Two transcript variants encoding different isoforms have been found for this gene.
Alias Symbols: EHHADH, ECHD,
Protein Size: 723 - Gene ID
- 1962
- NCBI Accession
- NP_001957
- UniProt
- Q08426
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