FKRP antibody (AA 237-265)

Catalog No. ABIN5536570

Product Details anti-FKRP Antibody

Target: FKRP (Fukutin Related Protein (FKRP))

Binding Specificity: AA 237-265

Reactivity: Human

Host: Rabbit

Clonality: Polyclonal

Conjugate: This FKRP antibody is un-conjugated

Application: Western Blotting (WB)

Purification: This antibody is purified through a protein A column, followed by peptide affinity purification.

Immunogen: This FKRP antibody is generated from rabbits immunized with a KLH conjugated synthetic peptide between 237-265 amino acids from the Central region of human FKRP.

Isotype: Ig Fraction

Application Details

Application Notes: For WB starting dilution is: 1:1000

Restrictions: For Research Use only

Handling

Format: Liquid

Concentration: 0.5 mg/mL

Buffer: Supplied in PBS with 0.09 % (W/V) sodium azide.

Preservative: Sodium azide

Precaution of Use: This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Storage: 4 °C,-20 °C

Storage Comment: Store at 4°C for three months and -20°C, stable for up to one year. As with all antibodies care should be taken to avoid repeated freeze thaw cycles. Antibodies should not be exposed to prolonged high temperatures.

Target Details for FKRP

Target: FKRP (Fukutin Related Protein (FKRP))

Alternative Name: FKRP (FKRP Products)

Synonyms: zgc:162829 antibody, LGMD2I antibody, MDC1C antibody, MDDGA5 antibody, MDDGB5 antibody, MDDGC5 antibody, A830029B19Rik antibody, AI842067 antibody, AI847300 antibody, LGMD1I antibody, fukutin related protein antibody, FKRP antibody, fkrp antibody, Fkrp antibody

Background: This gene encodes a protein which is targeted to the medial Golgi apparatus and is necessary for posttranslational modification of dystroglycan. Mutations in this gene have been associated with congenital muscular dystrophy, mental retardation, and cerebellar cysts. Several alternatively spliced transcript variants of this gene have been described, but the full-length nature of some of these variants has not been determined. [provided by RefSeq].

Molecular Weight: 55 kDa

Gene ID: 79147

UniProt: Q9H9S5

Pathways: Regulation of Carbohydrate Metabolic Process