COX6B1 antibody (AA 1-86)

Catalog No. ABIN7149179

Product Details anti-COX6B1 Antibody

Target: COX6B1 (Cytochrome C Oxidase Subunit VIb Polypeptide 1 (Ubiquitous) (COX6B1))

Binding Specificity: AA 1-86

Reactivity: Human

Host: Rabbit

Clonality: Polyclonal

Conjugate: This COX6B1 antibody is un-conjugated

Application: ELISA, Immunofluorescence (IF)

Cross-Reactivity: Human

Purification: >95%, Protein G purified

Immunogen: Recombinant Human Cytochrome c oxidase subunit 6B1 protein (1-86AA)

Isotype: IgG

Application Details

Application Notes: Recommended dilution: IF:1:50-1:200,

Restrictions: For Research Use only

Handling

Format: Liquid

Buffer: Preservative: 0.03 % Proclin 300
Constituents: 50 % Glycerol, 0.01M PBS, PH 7.4

Preservative: ProClin

Precaution of Use: This product contains ProClin: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Storage: -20 °C,-80 °C

Storage Comment: Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.

Target Details for COX6B1

Target: COX6B1 (Cytochrome C Oxidase Subunit VIb Polypeptide 1 (Ubiquitous) (COX6B1))

Alternative Name: COX6B1 (COX6B1 Products)

Synonyms: COX6B antibody, COXG antibody, COXVIb1 antibody, cox6b antibody, cox6b1 antibody, cox6b1a antibody, coxg antibody, coxvib1 antibody, 2010000G05Rik antibody, Cox6b antibody, RGD1565270 antibody, Cox6b1 antibody, fa92g05 antibody, si:dkey-161j23.2 antibody, wu:fa92g05 antibody, zgc:92631 antibody, COX VIb-1 antibody, COX6B1 antibody, cytochrome c oxidase subunit Vib polypeptide 1 (ubiquitous) antibody, cytochrome c oxidase subunit 6B1 antibody, cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous) L homeolog antibody, cytochrome c oxidase, subunit VIb polypeptide 1 antibody, cytochrome c oxidase subunit 6B antibody, cytochrome c oxidase subunit VIb polypeptide 1, pseudogene 1 antibody, cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous) antibody, COX6B protein antibody, cytochrome c oxidase subunit VIb polypeptide 1 antibody, COX6B1 antibody, cox6b1.L antibody, Cox6b1 antibody, Cox6b1-ps1 antibody, LOC100464665 antibody, COX6B antibody, cox6b1 antibody, LOC102143756 antibody

Background:

Background: Defects in COX6B1 are a cause of mitochondrial complex IV deficiency (MT-C4D) [MIM:220110], also known as cytochrome c oxidase deficiency. A disorder of the mitochondrial respiratory chain with heterogeneous clinical manifestations, ranging from isolated myopathy to severe multisystem disease affecting several tissues and organs. Features include hypertrophic cardiomyopathy, hepatomegaly and liver dysfunction, hypotonia, muscle weakness, excercise intolerance, developmental delay, delayed motor development and mental retardation. A subset of patients manifest Leigh syndrome.

Aliases: COX 6B antibody, COX VIb 1 antibody, COX VIb-1 antibody, COX6B antibody, COX6B1 antibody, COXG antibody, COXVIb1 antibody, CX6B1_HUMAN antibody, Cytochrome c oxidase subunit 6B1 antibody, Cytochrome c oxidase subunit VIb antibody, Cytochrome c oxidase subunit VIb isoform 1 antibody, cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous) antibody, Cytochrome c oxidase subunit Vib polypeptide 1 antibody

UniProt: P14854