PCCB antibody (AA 83-539)
Quick Overview for PCCB antibody (AA 83-539) (ABIN7876945)
Target
See all PCCB AntibodiesReactivity
Host
Clonality
Conjugate
Application
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Binding Specificity
- AA 83-539
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Purpose
- PCCB Antibody / Propionyl-CoA carboxylase beta chain
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Purification
- Antigen affinity purified
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Immunogen
- E. coli-derived recombinant human protein (amino acids D83-L539) was used as the immunogen for the PCCB antibody.
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Isotype
- IgG
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Application Notes
- Optimal dilution of the PCCB antibody should be determined by the researcher.
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Restrictions
- For Research Use only
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Format
- Lyophilized
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Buffer
- 0.5 mg/mL if reconstituted with 0.2 mL sterile DI water
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Storage
- 4 °C,-20 °C
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Storage Comment
- After reconstitution, the PCCB antibody can be stored for up to one month at 4oC. For long-term, aliquot and store at -20oC. Avoid repeated freezing and thawing.
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- PCCB (Propionyl CoA Carboxylase beta Polypeptide (PCCB))
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Alternative Name
- PCCB
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Background
- The protein encoded by this gene is a subunit of the propionyl-CoA carboxylase (PCC) enzyme, which is involved in the catabolism of propionyl-CoA. PCC is a mitochondrial enzyme that probably acts as a dodecamer of six alpha subunits and six beta subunits. This gene encodes the beta subunit of PCC. Defects in this gene are a cause of propionic acidemia type II (PA-2). Multiple transcript variants encoding different isoforms have been found for this gene.
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UniProt
- P05166
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Pathways
- Monocarboxylic Acid Catabolic Process
Target
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