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CLN6 Products

(Ceroid-Lipofuscinosis, Neuronal 6, Late Infantile, Variant (CLN6))

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This gene is one of eight which have been associated with neuronal ceroid lipofuscinoses (NCL). Also referred to as Batten disease, NCL comprises a class of autosomal recessive, neurodegenerative disorders affecting children. The genes responsible likely encode proteins involved in the degradation of post-translationally modified proteins in lysosomes. The primary defect in NCL disorders is thought to be associated with lysosomal storage function. [provided by RefSeq, Oct 2008].

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Featured CLN6 Categories

CLN6 Antibodies

High quality antibodies with extensive validation data.

CLN6 Proteins

Proteins for various applications incl. WB, ELISA, IF etc.

Recommended CLN6 Antibodies

Product
Reactivity
Application
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Application WB, ELISA, IHC
Validations
  • (2)
Cat. No. ABIN7183348
Quantity 100 μL
Datasheet Datasheet
Reactivity Human, Mouse, Rat
Application WB, ELISA, IHC, IF, ICC
Validations
  • (2)
Cat. No. ABIN6259070
Quantity 100 μL
Datasheet Datasheet
Reactivity Human
Application ELISA, IHC
Validations
  • (1)
Cat. No. ABIN7147497
Quantity 100 μg
Datasheet Datasheet

Recommended CLN6 ELISA Kits

Product
Reactivity
Analytical Method
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Analytical Method Quantitative Sandwich ELISA
Validations
Cat. No. ABIN6230888
Quantity 96 tests
Datasheet Datasheet

Recommended CLN6 Proteins

Product
Reactivity
Source
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Source Wheat germ
Validations
  • (1)
Cat. No. ABIN1349721
Quantity 10 μg
Datasheet Datasheet
Reactivity Human
Source Tobacco (Nicotiana tabacum)
Validations
Cat. No. ABIN3107550
Quantity 1 mg
Datasheet Datasheet
Reactivity Human
Source HEK-293 Cells
Validations
  • (1)
Cat. No. ABIN2712884
Quantity 20 μg
Datasheet Datasheet

Synonyms and alternative names related to CLN6

ceroid-lipofuscinosis, neuronal 6 (Cln6), CLN6, transmembrane ER protein (CLN6), CLN6, transmembrane ER protein S homeolog (cln6.S), ceroid-lipofuscinosis, neuronal 6, late infantile, variant (CLN6), CLN6, transmembrane ER protein (Cln6), CLN6, transmembrane ER protein a (cln6a), 1810065L06Rik, AW743417, CLN4A, cln6, D9Bwg1455e, HsT18960, nclf, zgc:103565

Protein level used designations for CLN6

  • neuronal ceroid lipofuscinosis
  • ceroid-lipofuscinosis neuronal protein 6
  • ceroid-lipofuscinosis neuronal protein 6 homolog
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