MMACHC antibody
-
- Target See all MMACHC Antibodies
- MMACHC (Methylmalonic Aciduria (Cobalamin Deficiency) CblC Type, with Homocystinuria (MMACHC))
-
Reactivity
- Human
-
Host
- Mouse
-
Clonality
- Monoclonal
-
Conjugate
- This MMACHC antibody is un-conjugated
-
Application
- Western Blotting (WB), Flow Cytometry (FACS)
- Characteristics
- Homo sapiens methylmalonic aciduria (cobalamin deficiency) cblC type, with homocystinuria (MMACHC)
- Purification
- Purified from mouse ascites fluids by affinity chromatography
- Immunogen
- Full length human recombinant protein of human MMACHC(NP_056321) produced in HEK293T cell.
- Clone
- 1B7
- Isotype
- IgG1
- Top Product
- Discover our top product MMACHC Primary Antibody
-
-
- Application Notes
- WB 1:2000, FLOW 1:100,
- Comment
-
The concentration of the product may vary between diferrent lots.
- Restrictions
- For Research Use only
-
- Format
- Liquid
- Concentration
- 0.5-1.0 mg/mL
- Buffer
- PBS (PH 7.3) containing 1 % BSA, 50 % glycerol and 0.02 % sodium azide.
- Preservative
- Sodium azide
- Precaution of Use
- This product contains sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
- Storage
- -20 °C
-
- Target
- MMACHC (Methylmalonic Aciduria (Cobalamin Deficiency) CblC Type, with Homocystinuria (MMACHC))
- Alternative Name
- MMACHC (MMACHC Products)
- Synonyms
- cblC antibody, RP11-291L19.3 antibody, RGD1310806 antibody, 1810037K07Rik antibody, methylmalonic aciduria (cobalamin deficiency) cblC type, with homocystinuria antibody, methylmalonic aciduria cblC type, with homocystinuria antibody, MMACHC antibody, Mmachc antibody
- Background
- The exact function of the protein encoded by this gene is not known, however, its C-terminal region shows similarity to TonB, a bacterial protein involved in energy transduction for cobalamin (vitamin B12) uptake. Hence, it is postulated that this protein may have a role in the binding and intracellular trafficking of cobalamin. Mutations in this gene are associated with methylmalonic aciduria and homocystinuria type cblC.
- Molecular Weight
- 31.5 kDa
- Gene ID
- 25974
- NCBI Accession
- NM_015506
- HGNC
- 25974
-