BSND antibody (Middle Region)
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- Target See all BSND Antibodies
- BSND (Bartter Syndrome, Infantile, with Sensorineural Deafness (Barttin) (BSND))
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Binding Specificity
- Middle Region
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Reactivity
- Human
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Host
- Rabbit
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Clonality
- Polyclonal
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Conjugate
- This BSND antibody is un-conjugated
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Application
- Western Blotting (WB)
- Sequence
- PNASPHDREE ACSPQQEPQG CRCPLDRFQD FALIDAPTLE DEPQEGQQWE
- Predicted Reactivity
- Human: 100%
- Characteristics
- This is a rabbit polyclonal antibody against BSND. It was validated on Western Blot.
- Purification
- Affinity Purified
- Immunogen
- The immunogen is a synthetic peptide directed towards the middle region of human BSND
- Top Product
- Discover our top product BSND Primary Antibody
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- Application Notes
- Optimal working dilutions should be determined experimentally by the investigator.
- Comment
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Antigen size: 320 AA
- Restrictions
- For Research Use only
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- Format
- Liquid
- Concentration
- Lot specific
- Buffer
- Liquid. Purified antibody supplied in 1x PBS buffer with 0.09 % (w/v) sodium azide and 2 % sucrose.
- Preservative
- Sodium azide
- Precaution of Use
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
- Handling Advice
- Avoid repeated freeze-thaw cycles.
- Storage
- -20 °C
- Storage Comment
- For short term use, store at 2-8°C up to 1 week. For long term storage, store at -20°C in small aliquots to prevent freeze-thaw cycles.
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- Target
- BSND (Bartter Syndrome, Infantile, with Sensorineural Deafness (Barttin) (BSND))
- Alternative Name
- BSND (BSND Products)
- Synonyms
- BSND antibody, BART antibody, DFNB73 antibody, Bartter syndrome, infantile, with sensorineural deafness (Barttin) antibody, barttin CLCNK type accessory beta subunit antibody, BSND antibody, Bsnd antibody
- Background
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This gene encodes an essential beta subunit for CLC chloride channels. These heteromeric channels localize to basolateral membranes of renal tubules and of potassium-secreting epithelia of the inner ear. Mutations in this gene have been associated with Bartter syndrome with sensorineural deafness.
Alias Symbols: BART, DFNB73, MGC119283, MGC119284, MGC119285
Protein Interaction Partner: FATE1, APP,
Protein Size: 320 - Molecular Weight
- 35 kDa
- Gene ID
- 7809
- NCBI Accession
- NM_057176, NP_476517
- UniProt
- Q8WZ55
- Pathways
- Sensory Perception of Sound
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