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BCKDHB antibody (N-Term)
BCKDHB
Reactivity: Human
WB, FACS, IF, IHC (p), EIA
Host: Rabbit
Polyclonal
unconjugated
Product Details anti-BCKDHB Antibody
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Target
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BCKDHB
(Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB))
Binding Specificity
All epitopes for BCKDHB antibodies
AA 44-74, N-Term
Reactivity
All reactivities for BCKDHB antibodies
Human
Host
All hosts for BCKDHB antibodies
Rabbit
Clonality
All clonalities for BCKDHB antibodies
Polyclonal
Conjugate
All conjugates for BCKDHB antibodies
This BCKDHB antibody is un-conjugated
Application
All applications for BCKDHB antibodies
Western Blotting (WB), Flow Cytometry (FACS), Immunofluorescence (IF), Immunohistochemistry (Paraffin-embedded Sections) (IHC (p)), Enzyme Immunoassay (EIA)
Specificity
This antibody reacts to BCKDHB.
Cross-Reactivity (Details)
Species reactivity (tested):Human.
Purification
Affinity chromatography on Protein A
Immunogen
KLH conjugated synthetic peptide between 44-74 amino acids from the N-terminal region of human BCKDHB
Isotype
Ig Fraction
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Discover our top product BCKDHB Primary Antibody
Alternatives
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Application Details
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Application Notes
Optimal working dilution should be determined by the investigator.
Restrictions
For Research Use only
Handling
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Format
Liquid
Concentration
0.25 mg/mL
Buffer
PBS containing 0.09 % (W/V) sodium azide as preservative
Preservative
Sodium azide
Precaution of Use
This product contains sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
Handling Advice
Avoid repeated freezing and thawing.
Storage
4 °C/-20 °C
Storage Comment
Store the antibody undiluted at 2-8 °C for one month or (in aliquots) at -20 °C for longer.
Target Details for BCKDHB
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Target
BCKDHB
(Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB))
Alternative Name
BCKDHB (BCKDHB Products )
Synonyms
zgc:158777 antibody, BCKDHB antibody, E1B antibody, dJ279A18.1 antibody, branched chain keto acid dehydrogenase E1, beta polypeptide antibody, branched chain keto acid dehydrogenase E1 subunit beta antibody, branched chain keto acid dehydrogenase E1, beta polypeptide S homeolog antibody, branched chain ketoacid dehydrogenase E1, beta polypeptide antibody, BCKDHB antibody, bckdhb antibody, bckdhb.S antibody, Bckdhb antibody
Background
Branched-chain keto acid dehydrogenase is a multienzyme complex associated with the inner membrane of mitochondria, and functions in the catabolism of branched-chain amino acids. The complex consists of multiple copies of 3 components: branched-chain alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2) and lipoamide dehydrogenase (E3). This gene encodes the E1 beta subunit, and mutations therein have been associated with maple syrup urine disease (MSUD), type 1B, a disease characterized by a maple syrup odor to the urine in addition to mental and physical retardation, and feeding problems.Synonyms: 2-oxoisovalerate dehydrogenase subunit beta, alpha-keto acid dehydrogenase, mitochondrial Branched-chain alpha-keto acid dehydrogenase E1 component beta chain
Gene ID
594
NCBI Accession
NP_000047
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