SGSH antibody (AA 318-466)
Quick Overview for SGSH antibody (AA 318-466) (ABIN1886363)
Target
See all SGSH AntibodiesReactivity
Host
Clonality
Conjugate
Application
-
-
Binding Specificity
- AA 318-466
-
Purification
- Purified by antigen-affinity chromatography.
-
Immunogen
- Recombinant protein fragment contain a sequence corresponding to a region within amino acids 318 and 466 of Human SGSH
-
-
-
-
Application Notes
-
Suggested dilutions:
Western blotting: 1.500-1.3000
Immunohistochemistry: 1.100-1.250 -
Restrictions
- For Research Use only
-
-
-
Format
- Liquid
-
Buffer
- 0.1 M Tris-buffered saline with 10 % Glycerol (pH 7.0).0.01 % Thimerosal was added as a preservative.
-
Preservative
- Thimerosal (Merthiolate)
-
Precaution of Use
- Biohazard Informations: This product contains thimerosal which is hazardous.
-
Storage
- 4 °C/-20 °C
-
Storage Comment
- Store at -20 °C for long term preservation (recommended). Store at 4 °C for short term use.
-
-
- SGSH (N-Sulfoglucosamine Sulfohydrolase (SGSH))
-
Alternative Name
- SGSH
-
Background
-
This gene encodes one of several enzymes involved in the lysosomal degradation of heparan sulfate.Mutations in this gene are associated with Sanfilippo syndrome A, one type of the lysosomal storage disease mucopolysaccaridosis III, which results from impaired degradation of heparan sulfate.Transcripts of varying sizes have been reported but their biological validity has not been determined.[provided by RefSeq]
-
Molecular Weight
- 57 kDa
-
Gene ID
- 6448
-
NCBI Accession
- NM_000199, NP_000190
-
Pathways
- Glycosaminoglycan Metabolic Process
Target
-