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FAH Products

(Fumarylacetoacetate Hydrolase (Fumarylacetoacetase) (FAH))
This gene encodes the last enzyme in the tyrosine catabolism pathway. FAH deficiency is associated with Type 1 hereditary tyrosinemia (HT). [provided by RefSeq, Jul 2008].

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Featured FAH Categories

FAH Antibodies

High quality antibodies with extensive validation data.

FAH ELISA Kits

Reliable ELISA kits for a wide range of species.

FAH Proteins

Proteins for various applications incl. WB, ELISA, IF etc.

Recommended FAH Antibodies

Product
Reactivity
Application
Validations
Cat. No.
Quantity
Datasheet
Reactivity Cow, Dog, Guinea Pig, Horse, Human, Mouse, Rabbit, Rat, Zebrafish (Danio rerio)
Application WB, IHC
Validations
  • (2)
  • (8)
Cat. No. ABIN2776935
Quantity 100 μL
Datasheet Datasheet
Reactivity Human, Mouse, Rat
Application WB, IHC
Validations
  • (5)
Cat. No. ABIN7257062
Quantity 200 μL
Datasheet Datasheet
Reactivity Human
Application WB
Validations
  • (5)
Cat. No. ABIN6140438
Quantity 100 μL
Datasheet Datasheet

Recommended FAH ELISA Kits

Product
Reactivity
Analytical Method
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Analytical Method Quantitative Sandwich ELISA
Validations
  • (5)
Cat. No. ABIN6574328
Quantity 96 tests
Datasheet Datasheet
Reactivity Mouse
Analytical Method
Validations
Cat. No. ABIN1133791
Quantity 96 tests
Datasheet Datasheet
Reactivity Cow
Analytical Method
Validations
Cat. No. ABIN1133789
Quantity 96 tests
Datasheet Datasheet

Recommended FAH Proteins

Product
Reactivity
Source
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Source Escherichia coli (E. coli)
Validations
  • (1)
Cat. No. ABIN7123017
Quantity 50 μg
Datasheet Datasheet
Reactivity Human
Source Wheat germ
Validations
  • (1)
Cat. No. ABIN1353376
Quantity 10 μg
Datasheet Datasheet
Reactivity Human
Source Wheat germ
Validations
  • (1)
Cat. No. ABIN1353378
Quantity 10 μg
Datasheet Datasheet

Latest Publications for our FAH products

Calattini, Fusil, Mancip, Dao Thi, Granier, Gadot, Scoazec, Zeisel, Baumert, Lavillette, Dreux, Cosset: "Functional and Biochemical Characterization of Hepatitis C Virus (HCV) Particles Produced in a Humanized Liver Mouse Model." in: The Journal of biological chemistry, Vol. 290, Issue 38, pp. 23173-87, (2015) (PubMed).

Qi, Li, Wang, Gao, Wang, Wei, Zhang, Sun, Tian: "Bone marrow transplantation concurrently reconstitutes donor liver and immune system across host species barrier in mice." in: PLoS ONE, Vol. 9, Issue 9, pp. e106791, (2014) (PubMed).

Hu, Lausted, Yoo, Yan, Brightman, Chen, Wang, Bu, Hood: "Quantitative liver-specific protein fingerprint in blood: a signature for hepatotoxicity." in: Theranostics, Vol. 4, Issue 2, pp. 215-28, (2014) (PubMed).

Wangensteen, Wilber, Keng, He, Matise, Wangensteen, Carson, Chen, Steer, McIvor, Largaespada, Wang, Ekker: "A facile method for somatic, lifelong manipulation of multiple genes in the mouse liver." in: Hepatology (Baltimore, Md.), Vol. 47, Issue 5, pp. 1714-24, (2008) (PubMed).

Synonyms and alternative names related to FAH

Fumarylacetoacetase (Faa), FumarylAcetoacetate Hydrolase (fah-1), fumarylacetoacetase (fahA), fumarylacetoacetase (hmgB), fumarylacetoacetase (Ndas_1870), fumarylacetoacetase (Lbys_3503), fumarylacetoacetase (Riean_0663), fumarylacetoacetase (Ftrac_0820), fumarylacetoacetase (Celal_3675), fumarylacetoacetase (Celly_2655), fumarylacetoacetase (Weevi_0208), fumarylacetoacetase (Fluta_2435), fumarylacetoacetase (Halhy_2019), fumarylacetoacetase (Lacal_2931), fumarylacetoacetase (FsymDg_1892), fumarylacetoacetate hydrolase (Fah), fumarylacetoacetate hydrolase (fumarylacetoacetase) (fah), fumarylacetoacetate hydrolase (fumarylacetoacetase) L homeolog (fah.L), fumarylacetoacetate hydrolase (FAH), fumarylacetoacetate hydrolase (fumarylacetoacetase) (FAH), CG14993, dfaa, Dmel\\CG14993, FAA, fb59b12, l(3)64Al, l(3)SH11, PSPTO3550, wu:fb59b12, zgc:55316

Protein level used designations for FAH

  • fumarylacetoacetase
  • CG14993-PA
  • Faa-PA
  • hypothetical protein
  • FAA
  • beta-diketonase
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