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GNS Products

(Glucosamine (N-Acetyl)-6-Sulfatase (GNS))

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The product of this gene is a lysosomal enzyme found in all cells. It is involved in the catabolism of heparin, heparan sulphate, and keratan sulphate. Deficiency of this enzyme results in the accumulation of undegraded substrate and the lysosomal storage disorder mucopolysaccharidosis type IIID (Sanfilippo D syndrome). Mucopolysaccharidosis type IIID is the least common of the four subtypes of Sanfilippo syndrome. [provided by RefSeq, Jul 2008].

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Featured GNS Categories

GNS Antibodies

High quality antibodies with extensive validation data.

GNS Proteins

Proteins for various applications incl. WB, ELISA, IF etc.

Recommended GNS Antibodies

Product
Reactivity
Application
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Application WB, IHC, ELISA
Validations
  • (3)
Cat. No. ABIN7160689
Quantity 100 μL
Datasheet Datasheet
Reactivity Human
Application WB, IHC (p), FACS
Validations
  • (3)
Cat. No. ABIN390493
Quantity 400 μL
Datasheet Datasheet
Reactivity Human
Application WB
Validations
  • (3)
Cat. No. ABIN950002
Quantity 100 μg
Datasheet Datasheet

Recommended GNS ELISA Kits

Product
Reactivity
Analytical Method
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Analytical Method Quantitative Sandwich ELISA
Validations
Cat. No. ABIN6730488
Quantity 96 tests
Datasheet Datasheet

Recommended GNS Proteins

Product
Reactivity
Source
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Source Wheat germ
Validations
  • (1)
Cat. No. ABIN1355451
Quantity 10 μg
Datasheet Datasheet
Reactivity Human
Source Wheat germ
Validations
  • (1)
Cat. No. ABIN1355450
Quantity 25 μg
Datasheet Datasheet
Reactivity Human
Source Insect Cells
Validations
  • (1)
Cat. No. ABIN3080899
Quantity 1 mg
Datasheet Datasheet

Synonyms and alternative names related to GNS

glucosamine (N-acetyl)-6-sulfatase (GNS), glucosamine (N-acetyl)-6-sulfatase (Gns), glucosamine (N-acetyl)-6-sulfatase S homeolog (gns.S), glucosamine (N-acetyl)-6-sulfatase (gns), glucosamine (N-acetyl)-6-sulfatase a (gnsa), N-acetylglucosamine-6-sulfatase (CpipJ_CPIJ000745), N-acetylglucosamine-6-sulfatase (Sros_7372), N-acetylglucosamine-6-sulfatase (VDBG_04409), N-acetylglucosamine-6-sulfatase (Halhy_3165), glucosamine (N-acetyl)-6-sulfatase (Sanfilippo disease IIID), b (gnsb), 2610016K11Rik, AU042285, C87209, G6S, gns, N-acetylglucosamine-6-sulfatase, N28088, NV14559, wu:fi20h10, zgc:55370, zgc:114066

Protein level used designations for GNS

  • N-acetylglucosamine-6-sulfatase
  • glucosamine-6-sulfatase
  • glucosamine (N-acetyl)-6-sulfatase (Sanfilippo disease IIID)
  • glucosamine (N-acetyl)-6-sulfatase
  • N-acetylglucosamine-6-sulfatase-like
  • n-acetylglucosamine-6-sulfatase-like
  • gnsl
  • glucosamine (N-acetyl)-6-sulfatase b
  • Glucosamine-6-sulfatase
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