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HPS4 Products

(Hermansky-Pudlak Syndrome 4 (HPS4))
This gene encodes a protein component of biogenesis of lysosome-related organelles complexes (BLOC). BLOC complexes are important for the formation of endosomal-lysosomal organelles such as melanosomes and platelet dense granules. Mutations in this gene result in subtype 4 of Hermansky-Pudlak syndrome, a form of albinism. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Aug 2012].

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Featured HPS4 Categories

HPS4 Antibodies

High quality antibodies with extensive validation data.

HPS4 ELISA Kits

Reliable ELISA kits for a wide range of species.

HPS4 Proteins

Proteins for various applications incl. WB, ELISA, IF etc.

Recommended HPS4 Antibodies

Product
Reactivity
Application
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Application WB, IHC, IP, ICC
Validations
  • (7)
Cat. No. ABIN7443911
Quantity 100 μL
Datasheet Datasheet
Reactivity Mouse
Application WB, IHC, IP, ICC
Validations
  • (5)
Cat. No. ABIN7443896
Quantity 100 μL
Datasheet Datasheet
Reactivity Human, Mouse, Rat
Application WB, IF
Validations
  • (3)
Cat. No. ABIN7258952
Quantity 200 μL
Datasheet Datasheet

Recommended HPS4 ELISA Kits

Product
Reactivity
Analytical Method
Validations
Cat. No.
Quantity
Datasheet
Reactivity Mouse
Analytical Method Quantitative Competition ELISA
Validations
Cat. No. ABIN1745638
Quantity 96 tests
Datasheet Datasheet
Reactivity Rat
Analytical Method Quantitative Competition ELISA
Validations
Cat. No. ABIN1744419
Quantity 96 tests
Datasheet Datasheet
Reactivity Monkey
Analytical Method Quantitative Competition ELISA
Validations
Cat. No. ABIN1770432
Quantity 96 tests
Datasheet Datasheet

Recommended HPS4 Proteins

Product
Reactivity
Source
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Source Insect Cells
Validations
  • (1)
Cat. No. ABIN3081654
Quantity 1 mg
Datasheet Datasheet
Reactivity Mouse
Source Insect Cells
Validations
  • (1)
Cat. No. ABIN3127932
Quantity 1 mg
Datasheet Datasheet
Reactivity Mouse
Source Escherichia coli (E. coli)
Validations
Cat. No. ABIN7417468
Quantity 100 μg
Datasheet Datasheet

Synonyms and alternative names related to HPS4

HPS4, biogenesis of lysosomal organelles complex 3 subunit 2 (HPS4), HPS4, biogenesis of lysosomal organelles complex 3 subunit 2 (Hps4), 2010205O06Rik, AU040608, BLOC-3, C130020P05Rik, LE, le, mKIAA1667

Protein level used designations for HPS4

  • Hermansky-Pudlak syndrome 4 protein
  • light-ear protein homolog
  • Hermansky-Pudlak syndrome 4 protein homolog
  • light ear
  • light-ear protein
  • Hermansky-Pudlak syndrome 4 homolog
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